Cumulative incidence of Kawasaki disease in Japan.

Background: Although the incidence rates of Kawasaki disease (KD) in Japan have been determined in nationwide surveys, the cumulative incidence, that is, the proportion of those with a history of KD in the general population of 10-year-olds, is currently unknown. The aim of this study was therefore to assess the cumulative incidence of KD in Japan.

Methods: Using the age- and sex-specific incidence rate of KD in Japan from the results of the nationwide surveys, incidence probabilities, that is, the age-specific number of KD patients divided by the population used in the vital statistics, and cumulative proportions of those not affected by KD up to the end of 9 years of age, were calculated.

[Relation between psychological development and respiratory management in patients with congenital central hypoventilation syndrome in Japan].

Objective: To evaluate the psychological development of patients with congenital central hypoventilation syndrome (CCHS).

Methods: We performed a questionnaire-based survey of 17 patients with CCHS aged over 7 years and assessed their clinical course, respiratory management, and psychological development.

Results: CCHS was present at birth in 15 patients, of which eight presented with respiratory failure with a low Apgar score.