[Moyamoya disease in a girl with Down syndrome. Report of one case].

Moyamoya disease is a unique chronic progressive cerebrovascular disease characterized by bilateral stenosis or occlusion of the arteries around the circle of Willis with prominent arterial collateral circulation. It can be primary or secondary to genetic syndromes such as Down syndrome. We report a seven year-old girl with a Down syndrome that presented with a disturbance of consciousness, seizures and a right hemiparesia at the age of five.

[Reversible posterior leukoencephalopathy syndrome in patients with immunosuppressive treatment: report of four cases].

Reversible posterior leukoencephalopathy syndrome (PLS) is characterized by headache, clouding of sensorium, visual disturbances and seizures. It is associated to hypertension, renal disease or immunosuppressive therapy. We report three males, aged 9, 12 and 16 years and one female, aged 5 years wih PLS associated to immunosuppressive therapy.

[Long-term continuous positive airway pressure (CPAP) use in obstructive sleep apnea].

Background: The use of CPAP is the conventional therapy for the Obstructive Sleep Apnea Syndrome (OSAS).

Aim: To establish the proportion of OSAS patients with CPAP indication who use it in the long-term and to determine predictive factors of adherence.

Patients And Methods: Structured survey through personal interview or phone call, applied to all patients who had polisomnographically documented OSAS and CPAP titration at the Pontificia Universidad Católica de Chile Sleep Disorders Center between January 1998 and November 2001.