Congenital dyserythropoietic anemia type II (CDA II), initially described as hereditary erythroblastic multinuclearity with a positive acidified serum test (HEMPAS), is a rare genetic disease inherited in an autosomal recessive mode that presents with mild to severe anemia. The occurrence of this entity is quite uncommon and requires extensive work-up for a conclusive diagnosis. Here, we are reporting a case of two-year-old male child who presented with severe anemia, abdominal distension, and delayed milestones.
View Article and Find Full Text PDFWaste tires have an organic-matter composition of more than 90% and have been proposed as an excellent calorific fuel material. The objective of this study is to find an economic and efficient pathway for producing syngas by waste tires gasification. To achieve this goal, two most commonly used gasifier types of fluidized bed and fixed bed have been simulated and compared by using a semi-empirical model and a one-dimensional kinetics model, respectively.
View Article and Find Full Text PDFThe Biomass Integrated Gasification Combined Cycle (BIGCC) power system is believed to potentially be a highly efficient way to utilize biomass to generate power. However, there is no comparative study of BIGCC systems that examines all the latest improvements for gasification agents, gas turbine combustion methods, and CO Capture and Storage options. This study examines the impact of recent advancements on BIGCC performance through exergy analysis using Aspen Plus.
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