The SPEC score-A quantifiable CT scoring system for primary ciliary dyskinesia.

Background: Structural lung changes seen on computed tomography (CT) scans in persons with primary ciliary dyskinesia (pwPCD) are currently described using cystic fibrosis (CF) derived scoring systems. Recent work has shown structural changes and frequencies that are unique to PCD, indicating the need for a unique PCD-derived scoring system.

Methods: Chest CT scans from 30 pwPCD, were described for structural changes including bronchiectasis, bronchial wall thickening, mucous plugging, atelectasis, air trapping, and interlobar septal thickening and, additionally, changes previously described as being frequent in pwPCD including extensive tree-in-bud pattern of mucous plugging, bronchoceles or nodules, thickening of interlobar and interlobular septa and whole lobe atelectasis.

Management of cutaneous side effects of inflammatory bowel disease therapy: A dermatologic viewpoint.

Medications used in the treatment of inflammatory bowel disease cause a wide range of dermatologic side effects, and minimal guidance exists on how to manage them. The intention of this review article is to summarize common dermatologic adverse reactions related to inflammatory bowel disease therapy and to provide evidence-based guidance on management. We conducted a scoping review using PubMed and Google Scholar to identify studies reporting clinical information on dermatologic side effects of medications used in the treatment of inflammatory bowel disease.

Social Media Use for Inflammatory Bowel Disease in a Rural Appalachian Population.

Social media use is prevalent in our society and has become widely used in the health care community. Inflammatory bowel disease (IBD) patients constitute one of the patient populations that benefit from social media use to obtain information on their diseases. West Virginia (WV) is a rural Appalachian state with barriers to internet access and health care and we examined the role that social media plays in patients' lives in this state, which could be reflective of other rural states.