Clear cell sarcoma of the kidney with inferior vena cava thrombus: a case report.

Background: Clear cell sarcoma of the kidney is an uncommon pediatric renal malignant neoplasm that is typically characterized in 2-3-year-olds by aggressive behavior and late relapses. Our literature review revealed fewer than ten previously reported cases of CCSK with inferior vena cava thrombus, with only five in the pediatric age group.

Case Presentation: We report the case of a 14-year-old Syrian girl who complained of mild pain in the left lumbar region pain with hematuria.