Cerebellar Cognitive Affective Syndrome in Costa da Morte Ataxia (SCA36).

SCA36 is an autosomal dominant spinocerebellar ataxia (SCA) affecting many families from Costa da Morte, a northwestern region of Spain. It is caused by an intronic GGCCTG repeat expansion in NOP56. In order to characterize the cognitive and affective manifestations of this cerebellar disease, a group of 30 SCA36 mutation carriers (11 preataxic and 19 ataxic patients) were assessed with a comprehensive battery of standardized tests.

Impact of subject's position and acoustic stimulus type on vestibular evoked myogenic potentials (VEMPs) in normal subjects.

Vestibular evoked myogenic potentials (VEMPs) are currently considered a diagnostic tool for studying the vestibular system, specifically the saccule and inferior vestibular nerve. This prospective study aimed at evaluating the impact of patient position and type of acoustic stimulus on VEMPs results using 60 healthy subjects who underwent otoscopy, pure tone audiometry and VEMPs in different conditions affecting their position and the type of acoustic stimulus. Corrected amplitude is significantly greater when the patient is seated and latency difference and amplitude asymmetry do not change with either patient position or type of stimulus.

Age-adjusted normality patterns for posturography by Sway Star system.

Technological advances have led to the development of new measurement techniques that have improved the evaluation, diagnosis, and treatment of patients with vertigo, dizziness and balance disorders. The objective of this study was to propose population normality patterns, adjusted for age, for summary option (balance control summary, BCS) of Sway Star system. Prospective study involving 70 healthy individuals (average age 44.

Benign paroxysmal positional vertigo of the posterior semicircular canal: efficacy of Santiago treatment protocol, long-term follow up and analysis of recurrence.

Objectives: To evaluate the efficacy of the Santiago treatment protocol for benign paroxysmal positional vertigo of the posterior semicircular canal, to analyse recurrence and to establish prognostic factors.

Material And Methods: Four hundred and twelve patients with unilateral benign paroxysmal positional vertigo of the posterior semicircular canal were treated with the Semont manoeuvre and, if symptoms did not resolve, successive application of three Epley manoeuvres plus Brandt-Daroff exercises.

Results: Symptoms resolved in 404 patients (98.

Comparative study of computerized dynamic posturography and the SwayStar system in healthy subjects.

Conclusions: For healthy subjects, posturography and SwayStar™ results are basically comparable, when they are obtained under the same sensory stimulation conditions. However, the management of the information and the mathematical analyses in the two systems are not comparable.

Objectives: Postural control represents man's ability to maintain the center of pressures inside the limits of stability.