Complete duplication of the bladder, urethra, vagina, and uterus in girls.

Unlabelled: OBJECTIVES. To present our experience with 3 girls with complete duplication of the bladder, urethra, vagina, and uterus, a very rare anomaly, and review published reports. Associated anomalies in these cases represent a wide spectrum.

[Congenital malformations of the genitourinary tract in children with Smith-Lemli-Opitz syndrome].

Smith-Lemli-Opitz (SLO) syndrome is an autosomal, recessive condition. The essence of SLO is abnormal metabolism of cholesterol which is characterized by decreased level of cholesterol and increased level of 7-dihydrocholesterol in serum. The main clinical features are mental retardation and congenital malformations of various organs and systems--microcephaly, syndactyly, craniofacial anomalies, cleft palate and genitourinary system, mainly external genitalia.

[Complete duplication of the urogenital system in girls].

The authors report 3 girls with complete duplication of the bladder, urethra, vagina and uterus. Defect's anatomy and associated anomalies are described. In support of the literature therapeutic procedure is discussed, which must be individualized in each case.

Bladder autoaugmentation in myelodysplastic children.

Objective: To present the long-term results of bladder autoaugmentation in myelodysplastic children with low compliance neurogenic bladders who failed attempts at medical management, including clean intermittent catheterization (CIC) and pharmacological bladder relaxation.

Patients And Methods: Twenty-one patients with a neurogenic bladder after myelomeningocele operations (mean age 9.5 years, range 3-16) underwent autoaugmentation; 12 children were paraplegic and hydrocephalic, and were treated by insertion of a ventriculoperitoneal valve.

[Cancer of the renal parenchyma in a 14-year-old girl with horseshoe kidney].

A 14-year-old girl is reported in whom carcinoma of the parenchyma of the right kidney and horseshoe kidney were diagnosed. The right kidney with the neoplasm was removed (carcinoma was in stage I of development), Histological examination demonstrated clear cell carcinoma. The patient remains under follow-up observation and two years after the operation she is well and no signs of disease have been observed.

[Surgical treatment of hermaphroditism in children (evaluation of surgical diagnostic procedures and surgical methods based on 56 treated cases)].

The author presented problems connected with surgical treatment of 56 hermaphrodite patients operated in Surgical Department of the Institute of Mother and Child in Warsaw. The classification of sexual abnormalities has been done in according to generally known pathological mechanisms of the external and internal genital organs development. Genital malformation may be due to presence of the abnormal pair of sex chromosomes, disturbed hormonal function of fetal testes, or suprarenal glands.