Publications by authors named "Sylvain Adam-Marchand"
Medicine (Baltimore)
November 2014
Article Synopsis
- Pulmonary fibrosis (PF) is an uncommon but severe complication found in patients with ANCA-associated vasculitis (AAV), especially in those with microscopic polyangiitis (MPA), and typically has a worse prognosis.
- In a study of 49 patients with PF and AAV, the majority were diagnosed with MPA, and 45% had PF appear before vasculitis symptoms, with usual interstitial pneumonia being the most common radiological pattern.
- Survival rates were higher in patients receiving combined therapy with glucocorticoids and immunosuppressants like cyclophosphamide, suggesting better treatment outcomes compared to glucocorticoids alone, emphasizing the importance of tailored therapy for these
