High Incidence of Sporadic Creutzfeldt-Jakob Disease in Slovenia in 2015: A Case Series.

Background: Creutzfeldt-Jakob disease (CJD) is a rare fatal neurodegenerative disorder presenting with rapid cognitive decline and additional signs. The clinical characteristics of an increasing number of sporadic CJD (sCJD) patients admitted to the Ljubljana University Medical Centre are presented as well as the incidence of sCJD in Slovenia in 2015 compared to previous years.

Methods: We investigated patients presenting with rapidly progressive dementia and at least one additional sign.