Long-term Prognosis of Mandibular Distraction in 3 Cases of Hypoglossia-Hypodactyly Syndrome without Extremity Anomalies.

Hypoglossia-hypodactyly, or aglossia-adactylia syndrome with or without limb anomalies, is an extremely rare congenital condition. It is characterized by a narrow, V-shaped mandibular dental arch with micrognathia, and is typically challenging to treat. We have previously reported 3 patients with hypoglossia-hypodactyly syndrome without limb anomalies who were treated with transverse distraction osteogenesis at the mandibular symphysis during childhood.

Midfacial Changes Through Anterior Maxillary Distraction Osteogenesis in Patients With Cleft Lip and Palate.

Maxillary hypoplasia is a major issue in cleft lip and palate patients, and predictable surgical maxillary advancement is required. In the present study, the changes and stability of the maxilla and soft tissue profile achieved after the application of anterior maxillary distraction osteogenesis (AMDO) using intraoral expander in unilateral cleft lip and palate and isolated cleft palate patients were investigated by comparing to the Le Fort I osteotomy (LFI) and maxillary distraction osteogenesis (DO) with rigid external distraction (RED) system.Ten patients who underwent orthognathic treatment with AMDO were examined (AMDO group).

Primary treatment for cleft lip and/or cleft palate in children in Japan.

Objective: To investigate current trends in primary treatment for children with cleft lip and/or cleft palate in Japan.

Design: Nationwide, retrospective study under the direction of the Academic Survey Committee of the Japanese Cleft Palate Association based on analysis of data obtained via a booklet-style questionnaire completed by institutions providing primary treatment for cleft lip and/or palate patients. PARTICIPANTS, PATIENTS: Patients were 4349 children undergoing primary repair for cleft lip and/or palate at 107 participating institutions between 1996 and 2000.

Midfacial changes through distraction osteogenesis using a rigid external distraction system with retention plates in cleft lip and palate patients.

Purpose: The purpose of this study was to investigate the changes in and stability of the maxilla and soft tissue profile achieved after the application of distraction osteogenesis (DO) by use of rigid external distraction (RED) with a retention plate system in unilateral cleft lip and palate (UCLP) adult patients. We compared 2 treatment methods in the management of maxillary hypoplasia: Le Fort I osteotomy and DO.

Materials And Methods: Six UCLP adult patients who underwent treatment with the RED retention plate system were examined (DO group).

Long-term follow-up of dental implants placed in a grafted alveolar cleft: evaluation of alveolar bone height.

Objective: The purpose of this study was to evaluate the long-term follow-up of dental implants placed in the grafted alveoli of patients with cleft lip or palate clinically.

Patients And Methods: Sixteen patients (8 males and 8 females) who had dental implants placed in alveoli grafted using particulate cancellous bone and marrow (PCBM) from the iliac crest were evaluated. The marginal bone level around the implant was evaluated radiologically at 1 (stage I), 3 (stage II), and 6 years (stage III) after connecting the abutment.

Rigid external distraction using skeletal anchorage to cleft maxilla united with alveolar bone grafting.

Objective: Documentation of the application of maxillary distraction osteogenesis using rigid external distraction (RED) with skeletal anchorage combined with predistraction alveolar bone grafting (ABG) in cleft maxilla.

Design: Case report.

Patient: A patient with numerous congenital missing teeth and severe maxillary deficiency related to complete bilateral cleft lip and palate with large alveolar bone defect.

Morphologic characteristics of masseter muscle in cleidocranial dysplasia: a report of 3 cases.

Cleidocranial dysplasia (CCD) is a rare autosomal dominant skeletal dysplasia. In order to define the morphologic characteristics of the masseter muscle incidental to bone abnormalities, we present 3 cases of CCD with the masseter muscle thickness and maxillofacial bone abnormalities, using computed tomography (CT) and panoramic radiographs. In CCD patients (a) the masseter muscles were less thick than in age- and sex-matched control subjects, (b) the zygomatic arch was discontinuous with the hypoplastic zygomatic bone, (c) the ascending ramus of the mandible had parallel-sided borders, and (d) the coronoid process pointed upwards and/or posteriorly.

Mandibular widening by distraction osteogenesis in the treatment of a constricted mandible and telescopic bite.

Objective: Documentation of the application of mandibular widening by distraction osteogenesis and orthodontics.

Patients: Three patients with telescopic bite resulting from an extremely constricted mandible related to hypoglossia-hypodactyly syndrome.

Intervention: Mandibular widening by distraction osteogenesis using an extraoral device and subsequent orthodontic treatment.

Alveolar ridge notching as a predictor for secondary bone grafting in incomplete alveolar clefts.

Objectives: To clarify the need for secondary alveolar bone grafting (ABG) in incomplete alveolar clefts identified clinically from its appearance and test the usefulness of alveolar ridge notching in the edentulous stage as a predictor for ABG.

Design: A prospective, cross-sectional study comparing three groups of patients at two stages.

Patients: Twenty-four patients with unilateral incomplete cleft of primary palate who underwent either no surgery or cheiloplasty only.

Characteristics of nonverbal behavior in patients with cleft lip and palate during interpersonal communication.

Objective: This study examined characteristics of nonverbal behavior that patients with cleft lip and palate (CLP) presented during interpersonal communication.

Design: This was a case-control design comparing nonverbal behavior of adult women with CLP with females without CLP.

Participants: Subjects were 20 adult women with CLP and 20 noncleft control women matched for age and educational experience.