[Clinical aspects and surgery of fibrocholangiocytosis in children].

Fifty one children with a diagnosis of fibrocholangiocystosis (FCC) were examined. A degree of circulatory blockade in the portal vein system in FCC was established to be one of the factors conditioning a severity of the course of the disease and its prognosis. With increase in duration of the disease and age of a child, the cirrhotic process in the liver and its complications are aggravating.

[Results of the surgical treatment of fibrocholangiocystosis of the liver in children].

A rare hereditary disease of the liver (fibrocholangiocystosis--congenital fibrosis of the liver) was surgically treated in 43 children. A conclusion is made that different palliative operations are inexpedient. Ilio-cavamesenterial anastomoses may be recommended for preventing relapses of gastroesophageal hemorrhages.