The association of Alagille syndrome and craniosynostosis.

Alagille syndrome is associated with various ocular abnormalities, including pseudopapilledema or optic disk edema due to increased intracranial pressure. Several mechanisms have been proposed to explain the mechanism of intracranial hypertension in Alagille syndrome. Craniosynostosis is an unusual but significant cause of increased intracranial hypertension in Alagille syndrome.

Fenestration methods for Sylvian arachnoid cysts--endoscopy or microsurgery.

Introduction: Two different approaches to fenestration, endoscopic and microsurgical, are in use for Sylvian arachnoid cysts (SACs), the most frequent among intracranial arachnoid cysts. We presented the clinical data and compared our results, with regard to technique and clinical success, with either microsurgical or neuroendoscopic fenestration of SACs.

Materials And Methods: Twenty-nine patients who subjected to cysto-cisternostomy by the same team, using either of the two methods, were studied retrospectively.

Cerebro-spinal fluid shunt revisions, importance of the symptoms and shunt structure.

Aim: CSF shunt failure is still a frequent problem in children. This prospective study was designed for focusing symptoms and reasons of shunt failure. We also especially focused on the mechanical reasons of shunt failure.

Atypical teratoid/rhabdoid tumor of the central nervous system: clinicopathologic and immunohistochemical features of four cases.

Background: Atypical teratoid/rhabdoid tumor (AT/RT) is a rare aggressive infantile neoplasm of uncertain origin. This study was performed to assess the clinicopathologic and immunohistochemical features of four AT/RT cases.

Case Reports: Two cases were male and two were female, and their ages ranged from 8 to 103 months.

Medulloblastoma: clinicopathologic evaluation of 42 pediatric cases.

Purpose: The aim of this study was to assess the prognostic value of MIB-1 and p53 in the pediatric medulloblastoma group.

Materials And Method: Forty-two pediatric medulloblastoma cases diagnosed in a single institution during the past 10 years were evaluated. Follow-up data were available for 35 patients.

Melanotic progonoma of the skull in infancy.

Introduction: Melanotic progonoma or melanotic neuroectodermal tumor is a rare tumor in infancy. This lesion has to be considered in the differential diagnosis of benign or malignant lesions of calvarium.

Case Report: The authors present a case of a 4-month-old infant with left retroauricular mass.

Endoscopic treatment of suprasellar arachnoid cysts.

Objective: Arachnoid cysts constitute 1% of all intracranial mass lesions not resulting from trauma. Suprasellar arachnoid cysts (SACs) are uncommon. Obstructive hydrocephalus is the most common cause of initial symptoms and occurs in almost 90% of the patients with suprasellar arachnoid cyst.

Craniopharyngiomas in children: Turkey experience.

Objectives: Craniopharyngiomas are the most frequently encountered suprasellar tumors in children. Although they have a benign histology, total resection without morbidity is very difficult.

Methods: We aimed to review the results of pediatric craniopharyngioma patients treated in eight institutions in Turkey.

Thrombosis and thrombophilebitis of the internal jugular vein as a very rare complication of the ventriculoatrial shunt.

A 21-year-old man presented with a sausage shaped mass lesion, located in the right anterolateral region of the neck. He had been operated on for hydrocephalus and thoraco-lumbar myelomeningocele at the age of 10 days and 2 months, respectively. Although he was asymptomatic at the age of 10 years, ventriculoatrial (VA) shunt was considered non-functional.

Radiotherapy-induced secondary cranial neoplasms in children.

Background: Secondary malignant neoplasms (SMN) in CNS tumor survivors has become problem of increasing concern over the last 20 years. These tumors usually occur in a different site from the primary brain tumor several years after treatment.

Case Report: We report secondary cranial malignant neoplasms in three patients who were treated with irradiation and chemotherapy for their primary brain tumors.

Single photon emission tomography following posterior fossa surgery in patients with and without mutism.

Materials And Methods: We designed a prospective study to investigate single photon emission tomography (SPECT) findings in patients with or without mutism who had undergone posterior fossa surgery. These patients had a (99m)Tc-hexamethylpropyleneamine oxime-SPECT scan postoperatively. SPECT was performed between the 1st and 2nd week after surgery.