Bilateral sensorineural hearing loss can significantly impact a person's quality of life, with autoimmune inner ear disease (AIED) being one of the rare causes.
AIED presents diagnostic challenges due to the absence of standard criteria, and the study reviewed 6 patients (3 male, 3 female) aged 24-35 who experienced rapid hearing loss associated with either primary AIED or systemic autoimmune diseases.
Treatment involved systemic and inner ear steroids, showing varied responses, highlighting the need for early hearing rehabilitation to improve patient outcomes.