Comparing the RETeval portable ERG device with more traditional tabletop ERG systems in normal subjects and selected retinopathies.

Purpose: Our study aimed to determine if ISCEV standard-like ERGs recorded with the LKC RETeval portable ERG unit compared to those obtained using the more traditional tabletop unit.

Methods: ERGs recorded from normal subjects and patients affected with retinal ON and OFF pathway anomalies were compared. Analysis included peak time and amplitude measurements as well as time-frequency domain analysis with the discrete wavelet transform of waveforms obtained with the two systems.

Organic visual loss measured by kinetic perimetry and retinal electrophysiology in children with functional amblyopia.

Purpose: To demonstrate an organic (retinal) amblyogenic defect in functional amblyopes not responding to treatment.

Methods: Twenty-four children (Mean age: 5.9 ± 1.

Ring analysis of multifocal oscillatory potentials (mfOPs) in cCSNB suggests near-normal ON-OFF pathways at the fovea only.

Purpose: To investigate the center-periphery distribution of ON and OFF retinal responses in complete congenital stationary night blindness (cCSNB).

Methods: Photopic full-field flash ERGs (photopic ffERGs) and OPs (photopic ffOPs) and slow m-sequence (to enhance OP prominence) mfERGs (and filtered mfOPs) evoked by a 37 hexagon stimulus array were recorded from normal subjects and cCSNB patients. Discrete wavelet transform (DWT) analysis of photopic ffERGs and mfERGs was also performed in order to assess the contribution of the ON and OFF retinal pathways (i.

Revealing a retinal facilitatory effect with the multifocal ERG.

Purpose: We have previously shown that the amplitude of the mfERG response obtained to a single (large) hexagon is significantly smaller than that obtained when summating all the mfERG responses evoked to an array of 7-61 hexagons covering the same retinal area. The purpose of this study was to confirm our initial findings in normal subjects of different ages and in selected patients.

Methods: Binocular mfERGs (1, 7, 19, 37 and 61 hexagon arrays; Espion V6.

Optic pathway gliomas in patients with neurofibromatosis type 1: follow-up of 44 patients.

Background: Children born with neurofibromatosis type 1 (NF1) have an increased risk of developing optic pathway gliomas (OPGs) during childhood. The aim of this study is to evaluate the clinical course of NF1 patients with OPGs at our institution with respect to visual and endocrinologic morbidity.

Methods: Retrospective case series of patients with OPGs and NF1 seen at the Montreal Children's Hospital, where screening imaging is performed on all NF1 patients.

Optimal compliance for amblyopia therapy: occlusion with a translucent tape on the lens.

Objective: To demonstrate that optimal compliance to amblyopia therapy and a better visual outcome can be achieved by occluding the lens over the preferred eye with a translucent tape.

Study Design: Prospective study of amblyopic children.

Participants: Eighty-four amblyopic children recruited from 2000 to 2006 at the Montreal Children's Vision Centre.

Acquired restrictive strabismus and high axial myopia: diagnosis and management.

Objective: This paper documents the clinical, ultrasound, magnetic resonance imaging (MRI), and anatomic characteristics of 6 patients with esohypotropia and high axial myopia. The results of strabismus surgery performed on these patients are evaluated.

Study Design: Retrospective cohort study.

Prevalence and severity of hypertensive retinopathy in children.

The National High Blood Pressure Education Program (NHBPEP) report recommends a retinal exam seeking evidence of target organ damage in hypertensive children. This study aimed to determine the prevalence and severity of hypertensive retinopathy among hypertensive children, evaluated by pediatric ophthalmologists in the "real world" clinical setting using direct ophthalmoscopy. The authors retrospectively reviewed the medical records of the 83 children diagnosed with hypertension by a pediatric nephrologist between 1999 and 2006.

Resolution of periodic alternating nystagmus after decompression for Chiari malformation.

Case Report: A 20-year-old female presented with horizontal jerk nystagmus, blurred vision, severe headaches, unsteady gait, and paresthesia. Magnetic resonance imaging revealed Chiari malformation I. Symptoms resolved after decompression of the posterior cranial fossa and removal of the right cerebellar tonsil.

The photopic ERG luminance-response function (photopic hill): method of analysis and clinical application.

With progressively brighter stimuli, the amplitude of the photopic b-wave first increases, briefly saturates and then decreases gradually to reach a plateau, where the amplitude of the b-wave equals that of the a-wave; a phenomenon previously presented as the photopic hill. The unique presentation of this luminance-response function seriously complicates its analysis with curve fitting equations such as that of Naka-Rushton used for scotopic electroretinogram. We report a method of analysis of the photopic hill based on easily identifiable and reproducible features of the ascending and descending limbs of this function.

Ophthalmic complications of slit-ventricle syndrome in children.

Objective: To present the ophthalmic features and visual prognosis of patients with slit-ventricle syndrome (SVS).

Design: Observational case series.

Participants: Six patients diagnosed and treated with SVS at the Montreal Children's Hospital between 1985 and 1999.