Development and validation of a WHO ICF compliant hand and upper limb assessment tool for children: The Reach Out questionnaire.

Background: Current tools for evaluating hand and upper limb function in children do not represent all domains of the World Health Organization International Classification of Disability, Functioning and Health (ICF) framework and may not capture an accurate progression or regression of function over time.

Purpose: Based on this framework, we have developed an assessment tool (Reach Out) to evaluate function in children aged from 2 to 16 years following consultation with an advisory panel of specialists.

Study Design: Primary clinical study.

Subjective and Objective Assessment of Hand Function in Mucopolysaccharidosis IVa Patients.

Introduction: Morquio A is classically described as a skeletal dysplasia, but the impact of the abnormalities on the upper limb has not been described.

Aim: The aim of our study is to assess the level of subjective and objective functions of the hand and upper limb in Morquio A patients in order to advance understanding as this may change future management for this complex group of patients.

Method: We have evaluated a series of ten patients with Morquio syndrome who are currently part of the enzyme replacement therapy trials in our unit.

Early tendon transfer after wide resection of an undifferentiated sarcoma of the forearm in a neonate: a case report.

A 1-month-old female baby was diagnosed with an undifferentiated sarcoma of her forearm after incisional biopsy. She received five cycles of chemotherapy before a wide resection of her extensor muscles including the radial nerve was undertaken, resulting in a complete drop of wrist and fingers. At this stage, primary tendon transfer of the brachioradialis to extensor carpi radial brevis muscle was performed, which proved to be not sufficient.