[Orbital rhabdomyosarcoma in a 9-month-old baby].

A 9-month-old baby, born within the normal period of gestation and with normal psychomotor development, presented with a rapidly progressive small swelling persisting for several months and evolving towards an inflammatory status. CT scan of the orbit and brain after contrast injection showed right intraorbital tissue mass forcing the eyeball upwards and outwards. The patient underwent surgical biopsy of the lesion.

Diagnostic pitfall: primary myoepithelial carcinoma of the lacrimal gland, case report and literature review.

Background: In lacrimal gland, lymphomas and inflammatory lesions predominate. Primary epithelial tumours represent less than 30% of lacrimal gland lesions. Myoepithelial carcinoma of lacrimal gland is rare.

[A rare case of ocular scarrings in a patient with Vogt-Koyanagi-Harada disease].

We here report the case of a 27-year old patient, followed-up in our Department for treatment of chronic Vogt-Koyanagi-Harada disease ( VKH disease). Fundus examination showed depigmentation of the retinal pigment epithelium and of the choroid, appearing as a pseudotumoral peripapillary lesion. Vogt-Koyanagi-Harada disease is a multisystem disorder, characterized by bilateral granulomatous panuveitis with serous exudative multifocal retinal detachment.

[Usher syndrome: about a case].

Usher syndrome is a genetic disease resulting in double sensory deprivation (auditory and visual) called deafblindness. We report the case of a 50-year old patient, born to consanguineous parents, presenting with congenital deafness associated with normal vestibular function and pigmentary retinopathy responsible for decreased bilateral visual acuity occurred at the age of 16 years. This association composes Usher syndrome type 2, a rare autosomal recessive disorder.

[Unusual complication of radiation therapy, corneal perforation: about a case].

Radiation-induced ocular complications are common during radiation therapy for cancers of the head and neck. Some are mild and transient, others can be very serious jeopardizing visual function. This rare and unusual case study aims to highlight the different clinical manifestations and the ocular but especially corneal complications associated with radiation therapy as well as the diagnostic and therapeutic procedures of a corneal perforation which is a serious complication of radiation therapy.

[Conjunctival granuloma following neglected thorn injury: about a case].

It is sometimes difficult to detect a plant intraocular foreign body, mostly in cases where the history of ocular trauma is unclear, or in patients who consult several months after the trauma. We report a rare case of a 7 year old child with self inflicted trauma of the the left eye by a cactus thorn 3 months before admission, which resulted in a temporal conjunctival granuloma with higher inflammatory reaction of the anterior segment. Surgical exploration was performed allowing the extraction of the thorn with total excision of the granuloma.

[Role of oral antiviral therapy in the treatment of acute retinal necrosis].

Unlabelled: Acute retinal necrosis syndrome (ARNS) is a rare but devastating uveitic syndrome with devastating visual outcome (visual prognosis ++). It should be diagnosed as early as possible because of its severity and its risk of bilateralization. This is a rare entity caused by the group of herpes viruses.

Primary atypical teratoid/rhabdoid tumor of the optic nerve: a rare entity in an exceptional location.

Unlabelled: Atypical teratoid/rhabdoid tumors are rare and highly malignant central nervous system tumors. They have no specific radiological features and often present several histological components that make a problem in differential diagnosis with medulloblastoma and primitive neuroectodermal tumors. We present the case of a newborn girl complained of a gradual proptosis of the left eye secondary to an expansive lesional process of the optic nerve.