Smith-Magenis syndrome with Dandy-Walker malformation in a 2-year-old girl: A case report.

Smith-Magenis syndrome (SMS) and Dandy-Walker malformation (DWM) are uncommon genetic conditions with nonspecific clinical features, which makes reaching a definitive diagnosis challenging. We describe here, a 2-year-old girl who was diagnosed with SMS at the age of 12 months due to delayed growth and development. The child presented to hospital with acute heart failure and respiratory failure.

Influence of the Transducer-Mounting Method on the Radiation Performance of Acoustic Sources Used in Monopole Acoustic Logging While Drilling.

Transducers used in acoustic logging while drilling (ALWD) must be mounted on a drill collar, and their radiation performance is dependent on the employed mounting method. Herein, the complex transmitting voltage response of a while-drilling (WD) monopole acoustic source was calculated through finite-element harmonic-response analysis. Subsequently, the acoustic pressure waveform radiated by the source driven by a half-sine excitation voltage signal was calculated using the complex transmitting voltage response.

Human Occupancy Monitoring and Positioning with Speed-Responsive Adaptive Sliding Window Using an Infrared Thermal Array Sensor.

In the current era of advanced IoT technology, human occupancy monitoring and positioning technology is widely used in various scenarios. For example, it can optimize passenger flow in public transportation systems, enhance safety in large shopping malls, and adjust smart home devices based on the location and number of occupants for energy savings. Additionally, in homes requiring special care, it can provide timely assistance.

Influence of Heat- and Cold-Stressed Raw Milk on the Stability of UHT Milk.

This study investigated the variations and alterations in the concentrations of plasmin system components in raw and UHT (ultra-high-temperature) milk under cold stress (WCT ≤ -25 °C), heat stress (THI ≥ 80), and normal (THI < 70 and WCT ≥ -10 °C) circumstances. The findings indicated elevated amounts of plasmin system components in cold-stressed raw milk. While storing UHT milk at 25 °C, the concentrations and activity of plasmin in the milk exhibited an initial increase followed by a decrease, peaking around the 30th day.

A Method for Determining the Fracture Toughness of Shotcrete Materials Subjected to Freeze-Thaw Cycles.

Defects can be introduced into shotcrete materials after a few freeze-thaw cycles, which has a significant influence on the fracture performance of shotcrete. In this study, a series of shotcrete specimens with varying sizes, geometries, and initial crack lengths were prepared to investigate the fracture properties of notched shotcrete under freeze-thaw conditions. Considering the effects of specimen boundaries and material microstructure, a linear closed-form solution was proposed to determine the fracture toughness of frost-damaged shotcrete.