Primary Renal Synovial Sarcoma - A rare histology.

Renal tumours vary from a benign to highly malignant histology. Here we present a 54 yrs male with a heterogeneous large encapsulated cystic lesion in the right kidney upper pole showing areas of solid component and necrosis with no evidence of metastasis or paraneoplastic features. Post Right Radical Nephrectomy IHC, showed positive reaction for BCL-2, CD99 and vimentin, suggesting Primary Renal Synovial Sarcoma.