Long-term Outcomes of Staged Complete Repair of Pulmonary Atresia With Ventricular Septal Defect.

Background: The optimal strategy for pulmonary atresia with ventricular septal defect (PA-VSD) without major aortopulmonary collateral arteries is yet to be defined. It remains unclear how primary complete repair compares with staged repair.

Methods: This study reviewed the records of 107 patients with PA-VSD who were managed with systemic-to-pulmonary shunts from February 1989 to November 2019.

Poorer Self-Reported Physical Health and Higher Anxiety Trait in Young Adults With Previous Coarctation Repair.

Background: Little is known about the impact of a coarctation repair on the functional outcomes of young adults. This study aimed to determine (1) the functional and mental health status in young adults with previous coarctation repair, and (2) the impact of late hypertension on their quality of life.

Methods: A cross-sectional study using validated self-reported questionnaires (Short Form 36 version 2 [SF-36v2], Beck Depression Inventory [BDI], and State-Trait Anxiety Inventory [STAI]) was performed in 54 patients aged 15-47 years with previous paediatric coarctation repair.

Propensity Score Matched Analysis of Cleft Closure in Complete Atrioventricular Septal Defect Repair.

Background: Repair of complete atrioventricular septal defect (cAVSD) is achieved with low mortality. However, there is a high rate of reoperation on the left atrioventricular valve (LAVV), which is often attributed to nonclosure of the cleft. Although nonclosure of the cleft has been reported to be a risk factor for reoperation, no randomized controlled or propensity-matched trials have ever been performed.

Arterial Switch Operation in Patients With Taussig-Bing Anomaly and Aortic Arch Obstruction.

Background: Arterial switch operation (ASO) in children with Taussig-Bing anomaly and associated aortic arch obstruction (AAO) is technically demanding. This study sought to determine outcomes of patients with Taussig-Bing anomaly and AAO who underwent ASO at a single institution.

Methods: From 1983 to 2015, 844 patients underwent an ASO for biventricular repair at The Royal Children's Hospital.

Aortic valve repair in children without use of a patch.

Background: We aimed to assess the long-term outcomes of children in whom the aortic valve could be repaired without the use of patch material. We hypothesized that if the aortic valve is of sufficiently good quality to perform repair without patches, a durable repair could be achieved.

Methods: All children (n = 102) who underwent aortic valve repair without the use of a patch between 1980 and 2016 were reviewed.

Surgery for Truncus Arteriosus: Contemporary Practice.

Surgery for truncus arteriosus has an early mortality of 3% to 20%, with a long-term survival of approximately 75% at 20 years. Nowadays, truncus arteriosus repair is mostly done in the neonatal period together with a single-staged repair of concomitant cardiovascular anomalies. There are many challenging subgroups of patients with truncus arteriosus, including those with clinically significant truncal valve insufficiency, an interrupted aortic arch, or a coronary artery anomaly.

Rare Association of an Intramural Coronary Artery and Truncus Arteriosus.

The association of truncus arteriosus (TA) and an intramural coronary artery is rare. Seven (7) patients had TA and an intramural coronary artery at the Royal Children's Hospital, Melbourne between 1996 and 2018. Four (4) patients underwent concomitant unroofing of their intramural coronary artery.

Outcomes of Interrupted Aortic Arch Repair in Children With Biventricular Circulation.

Background: To evaluate the outcomes after surgical repair of interrupted aortic arch in patients with biventricular circulation.

Methods: We reviewed all children from a single institution (N = 177) who had interrupted aortic arch repair between 1978 and 2018. Patients were separated into simple (n = 122) and complex (n = 55) group based on their concomitant anomalies.

Truncus arteriosus repair: A 40-year multicenter perspective.

Objective: To examine the long-term surgical outcomes of patients who underwent truncus arteriosus (TA) repair.

Methods: Between 1979 and 2018, a total of 255 patients underwent TA repair at 3 Australian hospitals. Data were obtained by review of medical records from initial admission until last cardiology follow-up.

The quadricuspid truncal valve: Surgical management and outcomes.

Objective: To determine the outcomes of patients with a quadricuspid truncal valve (TV) and durability of TV repair.

Method: We reviewed 56 patients with truncus arteriosus and a quadricuspid TV who underwent complete repair between 1979 and 2018.

Results: TV insufficiency was present in 39 patients (mild, n = 22; moderate, n = 14; and severe, n = 3).

Ross Operation in Children: 23-Year Experience From a Single Institution.

Background: Data on the long-term outcomes in children after the Ross operation are limited. This study aimed to assess the long-term outcomes in children who underwent the Ross operation at a single institution.

Methods: The study reviewed all children (n = 140) who underwent the Ross operation at the Royal Children's Hospital in Melbourne, Australia between 1995 and 2018.

Long-term quality of life in adults following truncus arteriosus repair.

Objectives: To date, few studies have assessed the quality of life following congenital cardiac surgery. In this study, we aimed at determining the quality of life after truncus arteriosus (TA) repair using the Short Form 36 questionnaire in adult survivors.

Methods: Seventy-three patients (age >18 years) who underwent TA repair at the Royal Children's Hospital, Australia were identified for the study.

Long-term outcomes following repair of truncus arteriosus and interrupted aortic arch.

Objectives: We aim to evaluate the long-term outcomes following repair of truncus arteriosus with an interrupted aortic arch.

Methods: We reviewed all children (n = 24) who underwent repair of truncus arteriosus and an interrupted aortic arch between 1979 and 2018 in a single institution. The morphology of the interrupted aortic arch was type A in 5, type B in 18 and type C in 1.

Impact of truncal valve surgery on the outcomes of the truncus arteriosus repair.

Objectives: Preoperative moderate or greater truncal valve (TV) insufficiency is one of the most important factors influencing mortality in children with truncus arteriosus. We therefore sought to determine the impact of TV insufficiency and concomitant TV surgery on children who underwent truncus arteriosus repair at a single institution.

Methods: We reviewed 180 patients who underwent truncus arteriosus repair between 1979 and 2016.