Chiari I malformation presenting with hearing loss: surgical treatment and literature review.

Objects: Chiari I malformations can present with a number of clinical signs and symptoms.

Methods: We present a case of an 11-year-old girl that presented with significant sensorineural hearing loss as her only Chiari-related symptom. The patient had four audiograms that all demonstrated progressive bilateral hearing loss between 10 and 30 dB.