Multi-site diagnosis and management of 260 patients with auditory neuropathy/dys-synchrony (auditory neuropathy spectrum disorder).

Test results and management data are summarized for 260 patients with diagnoses of Auditory Neuropathy Spectrum Disorder (ANSD). Hearing aids were tried in 85 of these patients, and 49 patients tried cochlear implants. Approximately 15% reported some benefit from hearing aids for language learning, while improvement in speech comprehension and language acquisition was reported in 85% of patients who were implanted.

Telemedicine-assisted neurotology in post-Katrina Southeast Louisiana.

Objective: This study evaluates technical requirements, privacy and legal constraints, reimbursement considerations, and overall feasibility of a new telemedicine neurotologic patient care delivery model in post-Katrina, Southeast Louisiana.

Methods: This study is a retrospective review of the first year of a telemedicine neurotology practice with limited on-site neurotology physician availability (3-days monthly) with a full-time on-site audiologist, a full-time specialty-trained nurse practitioner, full-time neurosurgery on-site availability, and full-time otolaryngology on-site availability.

Results: A combined "store-and-forward" and "real-time" telemedicine delivery model was implemented for a new neurotology practice.

Absent or elevated middle ear muscle reflexes in the presence of normal otoacoustic emissions: a universal finding in 136 cases of auditory neuropathy/dys-synchrony.

We extracted a subpopulation of 136 patients (from our database of 257 AN/AD subjects) in whom middle ear muscle reflexes had been measured. None showed normal reflexes at all frequencies tested. Only three subjects showed any reflexes at 95 dB HL or below, but never at both 1 and 2 kHz in both ears whether ipsilaterally or contralaterally elicited.