H Syndrome - A Case Report.

This case report describes a case of H syndrome with characteristic cutaneous hyperpigmentation, hypertrichosis, sclerodermatous thickening, and multisystem involvement such as hearing loss and heart anomaly in an Indian patient. There are around 100 cases of this rare, autosomal recessive genodermatosis reported in the literature, out of which 10 cases are from the Indian population. The aim of this paper is to increase awareness about this novel inherited form of histiocytosis and insist on the role of dermatologists to identify such patients in our population where consanguinity is prevalent.

The conundrum of parapsoriasis versus patch stage of mycosis fungoides.

Terminological confusion with benign dermatosis, such as parapsoriasis en plaques, makes it difficult to diagnose mycosis fungoides in the early patch stage. Early diagnosis of mycosis fungoides (MF) is important for deciding on type of therapy, prognosis and for further follow-up. However, until recently, there has been no consensus on criteria that would help in diagnosing the disease early.

Specific Skin Involvement in Leukaemias and Lymphomas.

Four cases of leukemia, 5 cases of non-Hodgkin's lymphoma and 3 cases of Hodgkin's lymphoma, developed maculo-papular rashes, papules, nodules, urticarial skin lesions and a plaque. Each of these on histopathology, showed a specific skin infiltrate corresponding to the malignancy.