[Peripheral ameloblastic fibrosarcoma].

We describe the clinicopathological features of a peripheral ameloblastic fibrosarcoma (PAFS) diagnosed in a 89-years-old man with a past history of recurrent peripheral ameloblastoma. Like other peripheral odontogenic tumors, PAFS shows histological features comparable to those of the central intraosseous form, with (fibro)sarcomatous proliferation associated to benign-appearing ameloblastomatous areas. The differential diagnosis must be made with a low-grade spindle ameloblastic carcinoma and with a collision tumor (a non odontogenic sarcoma associated with a recurrent ameloblastoma).