Publications by authors named "Pamela A Mazzeo"
Feeding and nutrition in children with medical complexity.
Curr Probl Pediatr Adolesc Health Care
September 2021
Providing adequate and appropriate nutrition to children with medical complexity (CMC) is often a challenging task. These patients are a diverse group whose varying nutritional needs must be carefully assessed and monitored. Optimal feeding and nutrition strategies in CMC require an individual approach and may include oral, enteral (gastric or jejunal), or parenteral provision of nutrients.
View Article and Find Full Text PDFArticle Synopsis
- Congenital disorders of glycosylation (CDGs) are genetic disorders that disrupt glycoprotein and glycolipid production, leading to various health issues, with ALG3-CDG being highlighted for its severe neurological and multisystem involvement.* -
- A study reported on 10 new cases of ALG3-CDG, identifying 11 novel genetic variants, increasing the total number of known cases to 40, and broadening the symptoms associated with this disorder to include endocrine issues, neural tube defects, and more.* -
- N-glycan analysis revealed distinct glycan deficiencies in these patients, which are characteristic of ALG3-CDG, indicating that a thorough evaluation of endocrine, renal, cardiac, and immun
The Poet׳s Obligation (The Problem of a "Calling").
Curr Probl Pediatr Adolesc Health Care
March 2020
Background: Alternate waiting list strategies have been promoted as a means to offer the benefit of heart transplantation to a greater number of candidates. We undertook the current study to evaluate our experience with transplantation in alternate list (AL) candidates.
Methods: Adults undergoing heart transplantation from January 1, 2001, through April 15, 2004, were evaluated.
Background: Conventional cardiopulmonary bypass results in cerebral ischemic sequelae that may be reduced with hybrid pump technologies, such as the CardioVention system (CardioVention, Santa Clara, CA, USA). CardioVention differs from conventional bypass in that it has a novel air elimination module and reduced membrane surface area and priming volume. This preliminary study tested whether this pump confers neurological safety advantages over conventional bypass.
View Article and Find Full Text PDFOver the last 6 years, 161 patients underwent implantation of HeartMate single-lead vented electric (SLVE) devices as a bridge to transplantation. SLVE patients were retrospectively analyzed before and after United Network for Organ Sharing (UNOS) policy changes, and designated SLVE-1 and SLVE-2, respectively. Mean support time decreased significantly from 79.
View Article and Find Full Text PDFObjective: Implantation of a left ventricular assist device as a bridge to transplantation has become an acceptable approach for patients with end-stage heart failure. Our long-term results with 3 Thoratec HeartMate devices are presented to outline improvements in successful bridging to transplantation and post-transplant survival.
Methods: From August 1990 through January 2003, 243 patients underwent implantation of Thoratec HeartMate devices as a bridge to transplantation.
Objectives: We evaluated the early and medium-term single-center results for primary repair of Ebstein anomaly in both adults and children.
Methods: The records were reviewed of patients undergoing repair of Ebstein anomaly at the Children's Hospital of New York from September 1990 to September 2002. Functional, demographic, and echocardiographic parameters were studied both preoperatively and postoperatively, along with functional status and adverse events.