Mauriac Syndrome: A Rare Hepatic Glycogenosis in Poorly Controlled Type 1 Diabetes.

Background: Hepatic glycogenosis (HG) is a complication of poorly controlled type 1 diabetes mellitus (T1DM), characterized by glycogen accumulation in hepatocytes. Mauriac syndrome (MS) is a glycogenic hepatopathy, initially described in 1930, characterized by growth failure, delayed puberty, cushingoid appearance, hepatomegaly with abnormal liver enzymes, and hypercholesterolemia. HG is a condition with good prognosis and fast resolution after adequate glycemic control (although it has potential for relapse), with no case of evolution to end-stage liver disease described.

People with patellofemoral pain have impaired functional performance, that is correlated to hip muscle capacity.

Objective: To (i) compare objective function in a range of tasks between people with and without patellofemoral pain (PFP); and (ii) evaluate the relationship of objective function with hip muscle capacity and self-reported function in people with PFP.

Design: Cross-sectional.

Settings: Laboratory.

Use of pregnancy-associated plasma protein-A during oocyte in vitro maturation increases IGF-1 and affects the transcriptional profile of cumulus cells and embryos from Nelore cows.

Insulin-like growth factor 1 (IGF-1) activity is established by the regulation of IGF binding protein activity, which blocks IGF-1 functions, whereas pregnancy-associated plasma protein-A (PAPP-A) improves IGF-1 bioavailability and facilitates binding to IGF receptors. To further extend our understanding of the effect of exogenous PAPP-A on bovine embryo production, we added this protein during in vitro maturation of cumulus-oocyte complexes (COCs); moreover, we assessed its effects on IGF-1 quantity in the maturation medium, embryonic yield and postwarming survival, blastocyst quality, and transcript abundance. Bovine COCs were matured in a serum-free medium, either with PAPP-A supplementation (100 ng/ml) or without (control).

ARE CARIOGENIC BACTERIA THE MAJOR RISK FACTOR TO DENTAL CARIES IN PATIENTS WITH ULCERATIVE COLITIS?

Background: High prevalence of dental caries in ulcerative colitis (UC) has been attributed to diet and changes in salivary environment.

Objective: We aimed to characterize the prevalence of dental caries, salivary flow rates, salivary buffering capacity and cariogenic bacteria counts of Mutans streptococci and Lactobacillus spp and to evaluate their relationship with drug therapy, disease activity and duration.

Methods: A cross-sectional study was performed with UC patients followed in a tertiary center.

Promoting a Significant Increase in the Photoluminescence Quantum Yield of Terbium(III) Complexes by Ligand Modification.

Two discrete mononuclear complexes, [Tb(bbpen)(NO)] () and [Tb(bbppn)(NO)] (), for which = -bis(2-hydroxybenzyl)--bis(pyridin-2-ylmethyl)ethylenediamine and = bis(2-hydroxylbenzyl)-bis(pyridin-2-ylmethyl)-1,2-propanediamine, were synthesized and characterized by FTIR, Raman, and photoluminescence (PL, steady-state and time-resolved modes) spectroscopy. The attachment of a methyl group to the ethylenediamine portion of the ligand backbone differentiates from and acts as a determining feature to both the structural and optical properties of the former. The single-crystal X-ray structure of is described here for the first time, while that of complex has been redetermined in the monoclinic 2 space group in light of new diffraction data.

Atypical Prader-Willi and 15q13.3 Microdeletion Syndromes in a Patient with an Unbalanced Translocation.

Prader-Willi syndrome (PWS) and recurrent 15q13.3 microdeletion syndrome can be caused by genomic rearrangements in the complex 15q11q13 chromosomal region. Here, we describe the first female child with PWS and 15q13.

Development of a highly sensitive xanthine oxidase-based biosensor for the determination of antioxidant capacity in Amazonian fruit samples.

The paper describes the development of an amperometric biosensor using Prussian Blue (PB) modified electrodes containing xanthine oxidase (XOD). The enzyme is immobilized by photo-polymerization into an azide-unit pendant water-soluble photopolymer (PVA-AWP). The parameters of the fabrication of the biosensor, XOD:PVA/AWP ratio, crosslinking irradiation time, and XOD charge, were optimized.

Beauveria bassiana (Ascomycota: Hypocreales)-treated Diamondback Moth (Lepidoptera: Plutellidae) Larvae Mediate the Preference and Functional Response of Euborellia annulipes (Dermaptera: Anisolabididae) Nymphs.

Biological control is one of the strategies to reduce populations of diamondback moth, Plutella xylostella (Linnaeus) (Lepidoptera: Plutellidae), the major pest of brassica. Entomopathogen-based biopesticides are recommended and used for its control, reducing the constant use of chemical pesticides. Predators and/or fungal entomopathogens have an increasing interest to be used against diamondback moth, and the compatibility of these control agents in the field is important for pest management.

Relationship between the architecture and function of ankle plantar flexors with Achilles tendon morphology in ballet dancers.

Achilles tendinopathy is the most frequent foot overuse injury in ballet dancers and knowledge of clinically modifiable factors related to tendon structure in a population at risk, such as ballet dancers, would be important for the development of preventive programs. Therefore, the present study aimed to assess relationships of gastrocnemius muscle architecture and ankle plantar flexors function with Achilles tendon morphology in ballet dancers. Fifty-four measures from 27 ballet dancers were collected.

The Effect of the Intra-gastric Balloon on Gastric Emptying and the DeMeester Score.

Background And Aims: The mechanism of weight loss with the intra-gastric balloon (IGB) is thought to be a decrease in gastric emptying (GE); however the evidence is conflicting. Nausea, abdominal pain, and gastroesophageal reflux disease (GERD) can cause intolerance resulting in early removal. This is demoralizing for the patient and costly for the healthcare system.

Vertical Ground Reaction Force During a Water-Based Exercise Performed by Elderly Women: Equipment Use Effects.

: The present study aimed to compare the vertical ground reaction force responses during the performance of the stationary running water-based exercise with and without equipment at different cadences by elderly women. : Nineteen elderly women (age: 68.6 ± 5.

Crystal structures of binuclear complexes of gadolinium(III) and dysprosium(III) with oxalate bridges and chelating ,'-bis-(2-oxido-benz-yl)-,'-bis-(pyridin-2-ylmeth-yl)ethyl-enedi-amine (bbpen).

The reaction between mononuclear [(bbpen)Cl] [ = Gd or Dy; Hbbpen = ,'-bis-(2-hy-droxy-benz-yl)-,'-bis-(pyridin-2-ylmeth-yl)ethyl-enedi-amine, CHNO] and potassium oxalate monohydrate in water/methanol produced the solvated centrosymmetric isostructural binuclear (μ-oxalato)bis-{[,'-bis-(2-oxidobenzyl-κ)-,'-bis-(pyridin-2-ylmethyl-κ)ethyl-enedi-amine-κ ,']dilanthanide(III)}-methanol-water (1/4/4) complexes, [ (CHNO)(CO)]·4CHOH·4HO, with lanthanide(III) = gadolinium(III) ( = Gd) and dysprosium(III) ( = Dy), in high yields ( 70%) directly from the reaction mixtures. In both complexes, the lanthanide ion is eight-coordinate and adopts a distorted square-anti-prismatic coordination environment. The triclinic ( ) unit cell contains one dimeric unit together with four water and four methanol mol-ecules; in the final structural model, two of each type of solvating mol-ecule refine well.

Acute Effects of Hip Mobilization With Movement Technique on Pain and Biomechanics in Females With Patellofemoral Pain: A Randomized, Placebo-Controlled Trial.

Context: People with patellofemoral pain (PFP) present altered lower-limb movements during some activities. Perhaps, joint misalignment in the hip is one of the reasons for altered movement patterns in people with PFP. Some mobilization techniques have been designed to address joint misalignments.

Multivariate analysis reveals significant diuron-related changes in the soil composition of different Brazilian regions.

Sorption and desorption determine the amount of an herbicide in soil solution. Therefore, knowledge of the sorption and desorption coefficients in different soils is an essential factor to estimate the potential for environmental contamination by herbicides. We evaluated the feasibility of multivariate and linear discriminant analyses to predict the sorption and desorption capacity of a soil for diuron, one of the most used herbicides on sugarcane plantations.

A proximal progressive resistance training program targeting strength and power is feasible in people with patellofemoral pain.

Objectives: To evaluate the feasibility of a 12-week progressive resistance training program for people with patellofemoral pain (PFP) targeting proximal muscle strength and power; and resulting clinical and muscle capacity outcomes.

Design: Feasibility study.

Setting: Clinical environment.

Boyd Amputation Using the Tension Band Technique.

Background: Amputation at the level of the hindfoot results in an equinus deformity from an imbalance of muscle-tendons acting across the ankle. Boyd's reconstruction for hindfoot amputations is a well-known technique that retains the calcaneus and fuses it with the distal tibia at the ankle mortise. It provides an excellent weight-bearing stump and in most cases does not require an artificial limb but its use has been restricted because of the difficulty in obtaining high union rates in the tibiocalcaneal fusion.