An exceptional case of urogenital sinus associated with a scrotal pouch and duplicate urethra in a female child.

We report the case of an unusual genitourinary anomaly in a 5-year-old patient. The malformation consisted of a para-anal persistent urogenital sinus in a 46XX patient associated with a scrotum-like structure in the presumed clitoral location. A duplicate urethra arising from the anterior aspect of the bladder neck drained into the scrotal pouch.

Duplicate bladder exstrophy: a unique variant.

Duplicate bladder exstrophy is an extremely rare congenital malformation. Two forms have been described, the anteroposterior form and the collateral form, which is the less common. We report a case of bladder exstrophy in association with a duplicated lower urinary tract, omphalocele, colic duplication and diphallia.

An unusual case of multilocular cystic nephroma with prominent renal pelvis involvement.

Multilocular cystic nephroma (MCN) is a relatively rare, benign tumor of uncertain etiology. It typically arises from the renal parenchyma and is often treated with nephrectomy. We report a case of MCN with unusual prominent renal pelvis extension.

[Xanthogranulomatous pyelonephritis in children].

Objective: The authors report their experience of xanthogranulomatous pyelonephritis in children and emphasize the diagnostic and therapeutic difficulties supported by several published series.

Materials And Methods: This was a retrospective based on ten patients treated for xanthogranulomatous pyelonephritis.

Results: Treatment was surgical in 90% of patients.

[Currarino's triad: anorectal malformation, sacral anomaly and presacral mass].

We report the case of a 3 year old boy with a combination of anorectal malformation, sacral agenesia and anterior meningocele (Currarino's triad) and provide a review of the literature of this rare syndrome.