Laparoscopic treatment of a cystic pheochromocytoma of 6cms: A challenging case.

Cystic pheochromocytoma is a very rare entity.Preoperative diagnosis is difficult because clinical, biochemical and radiologic findings are usually not consistent with a pheochromocytoma.Open surgery is traditionally the gold standard to avoid cyst rupture.

Left-sided congenital heart lesions in mosaic Turner syndrome.

In the era of the diseasomes and interactome networks, linking genetics with phenotypic traits in Turner syndrome should be studied thoroughly. As a part of this stratagem, mosaicism of both X and Y chromosome which is a common finding in TS and an evaluation of congenital heart diseases in the different situations of mosaic TS types, can be helpful in the identification of disturbed sex chromosomes, genes and signaling pathway actors. Here we report the case of a mosaic TS associated to four left-sided CHD, including BAV, COA, aortic aneurysms and dissections at an early age.

Primary renal angiosarcoma: Case report and literature review.

Angiosarcoma is a rare malignant tumour occurring in less than 2% of soft tissue sarcomas. Angiosarcoma involving the kidney usually represents metastasis from skin or visceral primary lesions, while angiosarcoma primarily occurring in the kidney is a very rare neoplasm. We report a case of angiosarcoma of the right kidney in a 59-year-old male.

Living and cadaver donor transplant programs in the Maghreb.

In the Maghreb, organ failure constitutes a major public health problem, especially given the increasing number of patients with chronic renal failure and the high cost of care. In this study, we attempted to seek the recommendations, through a questionnaire, of various officials related to organ transplantation as well as leaders of ethics committees and religious groups in different countries of the Maghreb. The objective was to improve the rate of organ donation and transplantation.

Cystic lymphangioma of the kidney: Diagnosis and management.

Introduction: Cystic lymphangioma is a rare benign vascular tumor that may arise in various sites, revealed at any age. Abdominal locations represent less than 10% of the cases preferentially involving the mesentery. We report a case of primary lymphangioma arising from the kidney.

Oncocytome de la surrénale : Étude de cas.

RéSUMé: Nous rapportons ici un nouveau cas de cette entité afin de souligner les caractéristiques anatomocliniques utiles à son identification et ceci, en vue de la distinguer des corticosurrénalomes, qui sont de pronostic nettement plus sombre.

Mucinous tubular and spindle cell carcinoma of the kidney associated with tuberculosis.

Mucinous tubular and spindle cell carcinomas (MTSCC) are low-grade renal epi-thelial neoplasms with approximately 100 documented cases reported in the literature. We report a case of MTSCC in a 79-year-old patient in association with a renal tuberculosis infection that has never been reported. Further investigations are needed to determine the frequency and true prognosis of these tumors.

Childhood nephrectomy indications: a changing profile.

Aim: To assess the changing profile of children's nephrectomy indications in the south of Tunisia during the last two decades.

Methods: There were 94 children who underwent nephrectomy between 1982 and 2007. They were classified into two groups.

Persistent Müllerian duct syndrome with torsion of a transverse testicular ectopia: first reported case.

Persistent Müllerian duct syndrome with transverse testicular ectopia is a rare pathologic association. A 7-month-old boy was admitted to the emergency department with a right testicular swelling. Physical examination revealed a tender right testis, the upper limits of which could not be palpated.

A transplant recipient with a mixed germ-cell ovarian tumor.

Immunosuppressed renal transplant recipients seem to be at significantly increased risk of developing neoplasms comparatively to nonimmunosuppressed individuals. A history of malignancy exposes the patient to a high risk for relapse after transplantation. We present a trans-plant recipient with a history of an ovarian mixed germ-cell tumor, with choriocarcinoma component, which was treated seven years prior to transplantation.

Ectopic adrenal cortex tissue: an incidental finding during inguinoscrotal operations in pediatric patients.

Objective: The aim of the present study was to assess the occurrence of ectopic remnants of adrenal cortex tissue encountered in pediatric patients who underwent groin surgical explorations.

Materials And Methods: We studied 1,862 patients with groin surgical explorations during a period of 12 consecutive years (1995-2006). Nodules resembling ectopic adrenal tissue were removed and the histopathological examination was performed using hematoxylin and eosin staining.

[Mitrofanoff appendicovesicostomy in children: indication and results].

Objective: To present the indications and short-term and long-term results of Mitrofanoff appendicovesicostomy in children.

Patients And Method: Between 1992 and 2004, 13 boys and 17 girls underwent Mitrofanoff appendicovesicostomy with creation of a stoma in the right iliac fossa. The mean age was 10 years (range: 5-15 years).

[Renal mucormycosis].

The authors report a case of disseminated mucormycosis presenting with left renal and muscular involvement in a 20-year-old immunocompetent man. The patient died rapidly before the diagnosis, established on histopathological examination of the nephrectomy specimen. This case illustrates the diagnostic difficulties and poor prognosis of this rare fungal infection.

Pure primary neuroendocrine tumor of the prostate: a rare entity.

An extrapulmonary neuroendocrine tumor arising in the prostate gland has been described in several case series; however, pure and primary prostatic neuroendocrine tumors are very rare, their biologic behavior is not yet well known, and there are only a few reports in the literature describing the clinical features and management of this neoplasm. This article presents the clinicopathologic findings of 2 patients presenting with this disease. The published reports of primary pure neuroendocrine prostate tumors are discussed.

[Appendiculoureteroplasty: about 6 cases].

Objective: Through this work we want to specify the place of ureteroappendiculoplasty as an important technical procedure for ureteral substitution.

Material And Methods: Between January 1997 and September 2002, 6 patients had an appendiculoureteroplasty.

Results: four women and two men with a mean age of 37 years (range 12 to 55 years) had a lesion of the right ureter.

Cytogenetics and fluorescence in situ hybridization assessment of sex-chromosome mosaicism in Klinefelter's syndrome.

A retrospective study was carried out in 152 infertile men to determine the prevalence of sex chromosome abnormalities among non-obstructive azoospermic and severe oligospermic men (n = 51) and to evaluate the feasibility of fluorescence in situ hybridization (FISH) techniques to assess mosaicism in Klinefelter's patients in comparison with conventional cytogenetics. Cytogenetic analysis were performed for 51 infertile men and among 14 chromosomal abnormalities found, nine were compatible with Klinefelter's syndrome. FISH staining with a CEP X/CEP Y probes were performed for Klinefelter's patients and for five of them; testes were biopsied for histopathologic examination.