Aim: Analyze the clinical and evolutive particularities of complete primary distal renal tubular acidosis in children,
Methods: We studied retrospectively 11 cases enrolled in the pediatrics department of Sousse during 10 years period (1993-2002).
Results: It is about 9 boys and 2 girls (sex-ratio = 45) aged 3 month to 5 years (mean age: 18 months). Diagnosis was suspected on clinical and biological data of presumption and confirmed by acidification test.