Publications by authors named "Michel Lemoine"

The dendrochemical approach holds significant promise for determining the geographical origin of wood as a complementary tool to dendroprovenancing based on tree-ring width. Tracing the origin of wood based on its elemental and isotopic composition is in particular interesting for provenance studies at the regional scale, as dendrochemical signatures are indicative of geological and pedological characteristics. Although, absorption of nutrients and trace elements reflects the composition of soil bioavailable pools, it is also modulated by multiple environmental and tree related factors.

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Article Synopsis
  • Cerebellar atrophy and hypoplasia, often detected through MRI in children with ataxia and developmental issues, are linked to leukodystrophies, which can affect brain myelin.
  • A recent study highlights two cases involving variants in the LSM7 gene: one child with a confirmed diagnosis and another with a presumed variant, suggesting LSM7's critical role in these conditions.
  • Our findings expand this understanding by presenting a new patient with similar symptoms and genetic variants in LSM7, reinforcing its association with neurodevelopmental disorders involving leukodystrophy and cerebellar atrophy.
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Mucopolysaccharidosis type I-H (MPS I-H) is a rare lysosomal storage disorder caused by α-L-Iduronidase deficiency. Early haematopoietic stem cell transplantation (HSCT) is the sole available therapeutic option to preserve neurocognitive functions. We report long-term follow-up (median 9 years, interquartile range 8-16.

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Although diploglossine osteoderms were mentioned in several systematic and paleontological studies, their morphological variability in single specimens or within species remains paradoxically undescribed. This is mainly the effect of the lack of attention paid hitherto to the morphological and histological characteristics of the tail osteoderms. This study demonstrated that a previously undescribed morphological variability exists in these osteoderms, especially in those resulting from tail regeneration.

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