Extraocular retinoblastoma in Indian children: clinical, imaging and histopathological features.

Aim: TO STUDY EYES WITH EXTRAOCULAR DISSEMINATION (EORB), WITH THE FOLLOWING AIMS: first to establish the mean lag period and to understand various reasons for delayed presentation, second to study their imaging profiles and third to analyze histopathological features of eyes enucleated after neoadjuvant chemotherapy.

Methods: Prospective study of clinical and imaging features of EORBs (stage III and IV International Retinoblastoma Staging System) presenting to a tertiary eye care centre. Histopathological features of eyes enucleated after receiving neoadjuvant chemotherapy were analyzed.

Congenital cystic eye: a clinicopathologic study.

Congenital cystic eye is an extremely rare congenital ocular anomaly where a cystic mass or neuroglial tissue replaces normal eyeball secondary to failure of invagination of the optic vesicle. The authors describe a case of a 13-year-old girl, including clinical, imaging, intraoperative, and histopathological findings of this uncommon malformation. In addition, it was associated with ectopic glial tissue in the brain, which is also a rare association of this anomaly.

Clinical and pathologic profile of angiomyxomas of the orbit.

Purpose: To describe clinical, imaging, and histopathologic features of angiomyxomas of the orbit, which are extremely rare tumors in the orbit.

Methods: A retrospective review of clinical case records and imaging findings of histopathologically diagnosed cases of angiomyxoma over a period of 8 years (2001-2008). The histopathologic features were studied by routine hematoxylin-eosin staining, special stain (Alcian blue), and immunohistochemistry.

Malignant non-teratoid medulloepithelioma of the optic nerve with intraocular extension.

Medulloepithelioma is an uncommon tumour. These tumours most commonly arise in the brain and spinal cord; however, they also may arise from the optic nerve. We, herein, report a rare case of malignant non-teratoid medulloepithelioma of the optic nerve with intraocular extension.

Congenital horizontal tarsal kink with microphthalmos corrected by intermarginal suture tarsorrhaphy.

Congenital horizontal tarsal kink is extremely rare. Only one case of associated microphthalmos has been reported. Various surgical techniques have been described with successful results.

Disseminated cysticercosis with multiple bilateral orbital cysts.

The authors report 2 cases of cysticercosis with widespread involvement of both orbits and subcutaneous tissue and muscles of the head, face, and neck. These cases highlight the severity of orbital involvement in patients with disseminated disease without signs of orbital infection. To the best of our knowledge, such an extensive involvement of both orbits has never been reported.

Simultaneous Occurrence of Glial Heterotopia and Meningocele in the Orbit with Clinical Anophthalmia and Neurological Anomalies.

The authors describe a 5-year-old boy who had three congenital anomalies (clinical anophthalmos, meningocele, and glial heterotopia) in the orbit. These were associated with multiple neurological anomalies.

Orbital schwannoma with cystic degeneration.

Background: Schwannoma is a benign, slowly growing, painless, peripheral nerve sheath tumour that is uncommon in orbit. Longstanding tumours may develop degenerative changes. Extensive cystic change in orbital schwannoma is quite rare.

Microbiological profile of donor corneas: a retrospective study from an eye bank in north India.

Purpose: To study the microbiological profile and the antibiotic sensitivity of the microorganisms cultured from donor corneas and evaluate with respect to the decontamination protocols during the study period.

Methods: Retrospective review of microbiological culture reports of 2,291 donor eyes sent from January 2000 to December 2003. Donor corneas were treated with 0.

Atypical synophthalmos with arhinencephaly unilateralis.

This article describes a rare case of a 4-month-old infant with atypical synophthalmos with ipsilateral arhinencephaly unilateralis, ethmoid sinus, and lacrimal apparatus and brain abnormalities--diagnosed on the basis of the clinical picture and imaging findings.

Atypical oculo-orbital complex choristoma in organoid nevus syndrome.

We report organoid nevus with left oculo-orbital choristoma fixing the globe in hypotropia, precanthal skin tag, and upper eyelid coloboma and right limbal dermoid. Computed tomography revealed a dilated lateral ventricle and cerebral atrophy. No neurologic deficit existed.