Introduction: Adult-onset asthma and periocular xanthogranuloma (AAPOX) is a rare non-Langerhans cell histiocytic disorder.
Aim: To describe the periocular clinical findings in a patient diagnosed with AAPOX, treated successfully by intralesional corticosteroids.
Case Report: A 40-year-old woman presented with bilateral eyelid swelling and adult-onset asthma.