Background: Aortic root abscess is a rare complication of infective endocarditis in children.
Case Report: A 5-year-old boy with infective endocarditis of aortic valve and an anterior aortic root abscess was found to have anomalous aortic origin of right coronary artery from the left coronary sinus on computed tomography scan with contrast.
Result: He was managed surgically by "patch and prosthesis" approach and required aortic root enlargement.