Hearing Rehabilitation through Bone-Conducted Sound Stimulation: Preliminary Results.

 The bone-anchored hearing aid (BAHA) is a bone conduction system that transmits the sound directly to the inner ear by surpassing the skin impedance and the subcutaneous tissue. It is indicated for patients with mixed, conductive and unilateral sensorineural hearing loss who did not benefit from conventional hearing aids (HAs). Although the benefits from BAHA are well demonstrated internationally, this field still lacks studies in Brazil.

Analysis of electrically evoked compound action potential of the auditory nerve in children with bilateral cochlear implants.

Introduction: The cochlear implant device has the capacity to measure the electrically evoked compound action potential of the auditory nerve. The neural response telemetry is used in order to measure the electrically evoked compound action potential of the auditory nerve.

Objective: To analyze the electrically evoked compound action potential, through the neural response telemetry, in children with bilateral cochlear implants.

Comparative analysis of vocabulary in children with cochlear implants.

Introduction: The use of tests assessing the speech of patients who underwent cochlear implant (CI) surgery is warranted to increase knowledge on the development of these patients' language skills. The ABFW Child Language Test evaluates vocabulary, phonology, fluency, and pragmatics and can be administered to these children.

Objective: To evaluate the vocabulary of children using CI.

Familial Alström syndrome: a rare cause of bilateral progressive hearing loss.

Introduction: Alström Syndrome is a rare disease caused by mutations in ALMS1 gene. It is characterized by a progressive degeneration of sensory functions, resulting in visual and audiological impairment, as well as metabolic disturbances such as childhood obesity, hyperinsulinemia, and diabetes mellitus type 2.

Objective: To report and discuss the genetic and audiological findings in two siblings with Alström syndrome.

Auditory neuropathy spectrum: the importance of adequate diagnosis.

Objective: To evaluate the prevalence of misdiagnosis of the hearing impaired children, in order to investigate the existence of Auditory Neuropathy Spectrum Disorder.

Methods: Analytical, prospective study conducted with 15 participants (30 ears) aged 10-12 years, with bilateral sensorineural hearing loss, attending a Hearing Rehabilitation Center, accompanied by a multidisciplinary team with otolaryngologist, audiologist, psychologist, teacher and social worker. The participants underwent ENT examination and audiological assessment: tympanometry, acoustic reflexes, otoacoustic emissions test and Auditory Evoked response.