A rare presentation of a large extra-abdominal desmoid tumor of the posterior neck and back.

Objective: To describe a difficult case of a large extra-abdominal desmoid fibroma of the posterior neck and back; to discuss the pathologic findings and treatment options of this case and to review the current literature for a rare presentation of this disease.

Method: A case report and review of the current relevant English literature, carried out using PubMed Medline, are presented.

Results: We present a challenging case in which a locally invasive desmoid of the posterior neck and back had grown to such an extent that complete surgical excision in one procedure was not possible.