Paraganglioma and phaeochromocytoma in adult Fontan patients.

Introduction: The purpose of this study was to address the gap in knowledge in the incidence, presentation and imaging features of PPGL in Fontan patients. It has been hypothesised in the literature that Fontan circulation patients have an increased incidence of these tumours. This study is the largest cohort of adult Fontan patients in North America.

Liver Imaging in Fontan Patients: How Does Ultrasound Compare to Cross-Sectional Imaging?

Background: Fontan patients frequently develop liver cirrhosis (LC); however, the diagnostic accuracy of ultrasound (US) for detecting LC and the clinical implications of such diagnoses have not been clearly established.

Objectives: This study aims to evaluate the diagnostic performance of US for detecting LC in an adult population with Fontan circulation and to determine the correlation between LC and mortality/transplantation.

Methods: This was a retrospective study.

Pregnancy Considerations in Tetralogy of Fallot.

The majority of women with repaired tetralogy of Fallot are able to tolerate pregnancy with a low risk of cardiovascular events. However, proactive contraceptive advice, prepregnancy counselling, and care by a pregnancy heart team with expertise in congenital heart disease are key to ensuring a good outcome for mother and baby. Maternal and fetal risks are increased in the presence of severe valvular stenosis, poorly tolerated arrhythmia, significant ventricular dysfunction, and cyanosis.