Single Ventricle Palliation in a Developing Sub-Saharan African Country: What Should be Improved?

Introduction: Single ventricle physiology management is challenging, especially in low-income countries.

Objective: To report the palliation outcomes of single ventricle patients in a developing African country.

Methods: We retrospectively studied 83 consecutive patients subjected to single ventricle palliation in a single center between March 2011 and December 2017.

A multinational and multidisciplinary approach to treat CHD in paediatric age in Angola: initial experience of a medical-surgical centre for children with heart disease in Angola.

Background: Epidemiological patterns of cardiac disease differ between developed countries and African nations. Despite the collaborative efforts of developed countries, several obstacles hinder the implementation of successful programmes for the management of children with heart disease in Africa. Materials and methods This study is a retrospective analysis of a bi-national two-institution partnership programme for the treatment of children with congenital and acquired heart disease.

Anomalous Origin of One Pulmonary Artery From the Ascending Aorta: From Diagnosis to Treatment in Angola.

Background: Anomalous origin of one pulmonary artery is a rare congenital heart disease in which one pulmonary artery branch originates from the ascending aorta.

Objective: To describe the experience of a cardiothoracic center in an African country to repair anomalous origin of one pulmonary artery in the context of Portugal-Angola collaboration.

Methods: Between March 2011 and March 2015, four consecutive patients with anomalous origin of pulmonary artery branch underwent surgical correction.

Ebstein's anomaly in children: a single-center study in Angola.

Introduction And Objective: Ebstein's anomaly is a rare complex congenital heart defect of the tricuspid valve. We aimed to describe the frequency, clinical profile, and early and short-term post-operative results in patients under the age of 18 years operated for this anomaly in a tertiary center in Angola.

Methods: A retrospective cross-sectional study was conducted over a period of 37 months.

Ebstein's anomaly: a case with an unexpected evolution.

Ebstein's anomaly of the tricuspid valve is a rare and complex congenital heart defect. Its etiology is unknown and in the majority of cases it is multifactorial. Mortality in the neonatal period is high.

Interrupted aortic arch: an eight-year experience.

Introduction: Interrupted aortic arch (IAA) is a rare congenital heart defect with a high mortality rate in the neonatal period. Surgical correction of associated intracardiac anomalies can be performed in a one-stage (primary) or two-stage approach.

Objectives: Case review of children with IAA operated in our center and to evaluate the surgical outcomes and the occurrence of complications.

[Neonatal lupus erythematosus].

Neonatal lupus erythematosus (NLE) is a rare immune disease. Clinical findings include congenital heart block (CHB), cutaneous manifestations, and hepatic and haematological abnormalities. The authors present a case of a baby with prenatal diagnosis of bradycardia.

Kawasaki disease.

Introduction: Kawasaki disease (KD) is the leading cause of acquired heart disease among children in developed nations. Its incidence has risen in recent years and 20% of untreated patients develop coronary artery abnormalities.

Objectives: To analyze the epidemiological, clinical, laboratory and echocardiographic data of cases diagnosed in Hospital Fernando Fonseca and to identify factors that may influence prognosis.