[Polymorphism of hereditary atypical spinal amyotrophy in adults].

The authors describe the clinical picture and morphological changes in the spinal cord and skeletal muscles associated with hereditary atypical spinal amyotrophy observed in adults living in the Saratov region. The intra- and interfamilial polymorphism of the disease and its prevalence in the region are considered.

[Myocardial lesions in several forms of progressive muscular atrophy].

Using the clinical, electrocardiographic, biochemical and morphological findings, the authors assessed the cardiovascular system in 30 patients with Duchenne's myopathy and spinal amyotrophy. An analysis of the material revealed considerable metabolic-dystrophic changes in the myocardium, being more pronounced with Duchenne's myopathy. The early diagnosis of myocardial damage in the above diseases can be made on the basis of evidence from the isoenzymic spectrum of creatine kinase.

[Hemodynamic disorders in the acute stage of stroke].

The state of hemodynamics was studied in the acute period of cerebral stroke in 84 hypertensive and atherosclerotic patients. A dependence of the hemodynamic shifts on the character of the stroke, the gravity of its clinical manifestations, time of the examination, and the disease outcome was demonstrated. On the basis of the data obtained individualized therapy is suggested.

[Polymorphism of Charcot-Marie-Tooth neural amyotrophy in uniovular twins].

The paper is concerned with a description of an atypical clinical picture of Charcot-Marie-Tooth neuronal amyotrophy in 2 eight-year old monozygotic twins. The traits of the disease were characterized by a deformation of the feet, mild cerebellar symptoms, development of ptosis and other myopathical symptoms, an enlargement of the transversal nerve of the neck and a distribution of the process to the proximal parts. The diagnosis was confirmed by EMG studies.