Neurological presentation of a congenital disorder of glycosylation CDG-Ia: implications for diagnosis and genetic counseling.

The congenital disorders of glycosylation (CDG) constitute a new group of recessively inherited metabolic disorders that are characterized biochemically by defective glycosylation of proteins. Several types have been identified. CDG-Ia, the most frequent type, is a multisystemic disorder affecting the nervous system and numerous organs including liver, kidney, heart, adipose tissue, bone, and genitalia.

A semi-automated data processing system for root growth analysis: application to a growing oak seedling.

A data acquisition and processing system for analyzing root structure and growth is presented. Two-dimensional drawings are made of root systems growing against the inclined, transparent wall of a rhizotron. For analysis, a root is treated as a number of straight segments between points determined by the position of root apices at successive times of observation and the insertion points of lateral roots.