Normal reference ranges for the left ventricular mass and left ventricular mass index in preterm infants.

Objective: The objective of this study is to establish normal reference ranges for the left ventricular mass (LVM) and LVM index (LVMI) in preterm infants according to the body surface area (BSA) and assess their correlation with body weight and gestational age.

Subjects And Methods: In a prospective study, 268 preterm babies who fulfilled the criteria for inclusion were examined. Echocardiograms were performed to measure the LVM and LVMI on 0-6 day (s) of life and at weekly intervals until the babies reached 36 weeks.

Long-term follow-up and outcomes of discrete subaortic stenosis resection in children.

Background: Studies of long-term outcomes of discrete subaortic stenosis (DSS) are rare. Therefore, we reviewed the long-term outcomes of subaortic membrane resection in children with isolated DSS over 16 years from a single institution.

Materials And Methods: We retrospectively reviewed the records of patients ( = 27) who underwent resection of DSS between 2000 and 2017.

Normal reference ranges for aortic diameters in preterm infants.

Objective: To establish normal reference ranges and -scores for aortic diameters in preterm infants according to the body surface area and assess their correlation with body weight, body surface area, and gestational age.

Patients And Methods: In a prospective study, 268 preterm infants who fulfilled the criteria for inclusion were examined. Echocardiograms were performed to measure the ascending aorta, transverse aorta, and aortic isthmus diameters on 0 days to 6 days of life and at weekly intervals until the babies reached 36 weeks.

Normal reference ranges for cardiac valve cross-sectional areas in preterm infants.

Objective: To establish normal reference ranges for cardiac valve crosssectional areas (CSAs) in preterm infants and their correlation with gestational age, body weight, and chronological age.

Materials And Methods: In a prospective study, 268 preterm babies fulfilling the criteria for inclusion were examined. Echocardiograms were performed to measure aortic, pulmonary, mitral, and tricuspid valve CSAs on 0-6 day (s) of life and at weekly intervals until they reached 36 weeks.

Normal Reference Ranges for Pulmonary Artery Diameters in Preterm Infants.

To establish normal reference ranges and Z-scores for pulmonary artery diameters in preterm infants and their correlation with body surface area, body weight, and chronological age. In a prospective study, 268 preterm infants, who fulfilled the inclusion criteria were examined. Echocardiograms were performed to measure the main pulmonary artery, right pulmonary artery, and left pulmonary artery diameters on day(s) 0 to -6 of life and at weekly intervals until they reached 36 weeks of age.

Normal Reference Ranges for Cardiac Valve Annulus in Preterm Infants.

Objective: The purpose of this study was to establish normal reference ranges for the cardiac valve annulus size in preterm infants and their correlation with gestational age, body weight and chronological age.

Subjects And Methods: In a prospective study, 268 pre-term babies, who fulfilled the criteria for inclusion, were examined in Kuwait during the years 2008-2010. Echocardiograms were performed to measure the aortic, pulmonary, mitral and tricuspid valve annulus size on 0-6 day(s) of life and at weekly intervals until they reached 36 weeks.

Normal reference ranges for left ventricular dimensions in preterm infants.

Objective: To establish normal reference ranges for the left ventricular dimensions in preterm infants and their correlation with gestational age, body weight and chronological age.

Materials And Methods: In a prospective study, 268 preterm babies, who fulfilled the criteria for inclusion, were examined in Kuwait during the years (2008-2010). Echocardiograms were performed to measure the left ventricular dimensions on 0-6 day(s) of life and at weekly intervals until they reached 36 weeks.

Occlusion of Fontan fenestrations using Amplatzer septal occluder.

The objective of the study is to assess efficacy and safety of the Amplatzer septal device for percutaneous occlusion of Fontan fenestration. Fenestration improves postoperative outcomes in children undergoing Fontan repair. Many of these fenestrations close spontaneously; persistent fenestrations ultimately cause desaturation and can be a potential cause of paradoxical embolism.

Novel TFAP2B mutation in nonsyndromic patent ductus arteriosus.

Mutations in the gene encoding the TFAP2B transcription factor can cause Char syndrome with cardiac, craniofacial, and hand abnormalities. However, TFAP2B mutations result in great phenotypic variability, which is believed to reflect different expression patterns of tissue-specific TFAP2 coactivators. We investigated a consanguineous family with isolated patent ductus arteriosus (PDA) for mutations in TFAP2B.

The impact of interruption of anomalous systemic arterial supply on scimitar syndrome presenting during infancy.

Objectives: We sought to evaluate the impact of interruption of anomalous systemic arterial supply (ASAS) on clinical course and management outcome of scimitar syndrome (SS) presenting during infancy.

Background: No systematic study has been reported so far on this subject, although there are conflicting sporadic reports indicating variable effect.

Methods: Out of 23 children diagnosed to have SS during the past 25 years, 16 symptomatic infants had ASAS.

Transcatheter closure of large pulmonary arteriovenous fistula including pulmonary artery to left atrial fistula with Amplatzer septal occluder.

Objectives: We sought to evaluate the safety and efficacy of Amplatzer septal occluder (ASO) to close very large pulmonary arteriovenous fistula (PAVF).

Background: Transcatheter coil embolization, the standard treatment for PAVF, has potential complications particularly in patients with very large fistulas. Several recently available devices have been tried effectively, however, they too have limitations.

Common arterial trunk associated with a homeodomain mutation of NKX2.6.

Persistent truncus arteriosus (PTA) is a failure of septation of the cardiac outflow tract (OFT) into the pulmonary artery and the aorta. A common arterial trunk (CAT) is often diagnosed as PTA in the absence of evidence of embryological mechanism. We have used autozygosity mapping of a large consanguineous family segregating CAT to map the causative locus to chromosome 8p21.

Transcatheter coil closure of pulmonary arteriovenous malformations in children.

Pulmonary arteriovenous fistula (PAVF) is a rare vascular malformation of the lung that may lead to cyanosis, epistaxis, hemoptysis, and neurological deficits or cerebral abscess. The purpose of this study is to assess the effectiveness of percutaneous transcatheter embolization of PAVF in pediatric patients. Transcatheter embolization of PAVF using spring coils was performed in three patients (two males and one female) who presented between 1989 and 1999.