Severe tricuspid stenosis during percutaneous occlusion of perimembranous ventricular septal defect with the new Amplatzer device.

Background: The new Amplatzer device has been used with success for occlusion of the perimembranous ventricular septal defects and the index of complications is very low.

Results: The reported case corresponds to a very rare severe acute tricuspid stenosis, caused by adherence of the prosthesis to the anterior tricuspid leaflet.

Conclusion: Device release was achieved by manipulation on the tricuspid apparatus.

Transcatheter closure of perimembranous ventricular septal defects.

The isolated perimembranous ventricular septal defect is one of the most common congenital cardiac malformations. Although surgery has been performed and has a low associated risk, it still involves morbidity due to factors such as residual leaks, atrioventricular block, postpericardiotomy syndrome and arrhythmias. It has been speculated that percutaneous closure of these defects could minimize such complications.

Noninvasive cardiac assessment in children of women with systemic lupus erythematosus.

Objective: Noninvasive cardiac assessment of newborns and infants of women with systemic lupus erythematosus. The children had no congenital total atrioventricular block and were compared with the children of healthy women.

Methods: We prospectively assessed 13 newborns and infants aged 1 to 60 days, children of women with systemic lupus erythematosus and without congenital total atrioventricular block.

Marfan's syndrome: early and severe form in siblings.

Marfan's syndrome is an inherited disorder of the connective tissue. Cardiologic manifestations, especially aortic dilation, are important causes of morbidity and mortality in the clinical course of the disease in adults and teenagers. In children, the presence of aortic aneurysm and its dissection or rupture is rare, occurring in patients with genetic mutation of the fibrillin gene but not in those who have the familial form of the disease.