[Comportamiento y decisión cardiovascular en el síndrome de MASS. Reporte de un caso y revisión de la literatura].

MASS syndrome (disorder of connective tissue characterized by involvement of the mitral valve, aorta, skeleton, and skin) is a rare genetic disease with a phenotype similar to that of Marfan syndrome, but with important cardiovascular differences like the absence of aortic root aneurysm and marked mitral affection. We present a case of a patient with MASS syndrome and review the limited literature addressing these differences, and we discuss the impact this information may have in decisions regarding cardiovascular surgery.

[Supraventricular tachycardial ablation supported with an electroanatomical system].

Unlabelled: In 1992 the radiofrequency ablation program was started, with very good results in patients with supraventricular tachycardias and normal hearts or minimal structural defects. Nevertheless, the results are not as good for the patients with structural defects, that are actually seen more frequently, those are cases with more complex arrhythmias, are patients with cardiac surgery that show a complex arrhythmogenic substrate or patients previously treated with conventional ablation which tachycardia recurs. In these cases, the electroanatomic Carto system has been very useful.

[Electrocardiogram in the differential diagnosis of wide-QRS tachycardias].

The surface ECG constitutes an invaluable tool for the differential diagnosis in those cases in which the QRS complex exceeds the normal duration (120 mseg or more) and a heart rate of 100 bpm or more. Most of the arrhythmias with wide QRS complexes are ventricular in origin, and frequently related to heart disease; nevertheless, in those patients with hemodynamic stability it is frequently misdiagnosed as supraventricular tachycardia. The importance of the surface ECG resides in the fact that the correct diagnosis can be done with high probability when the analysis is orderly made.

[Hypertrophic cardiomyopathy. Arrhythmia in hypertrophic cardiomyopathy].

Hypertrophic cardiomyopathy is a relatively common genetic disorder with heterogeneity in mutations, forms of presentation, prognosis and treatment strategies. Hypertrophic cardiomyopathy is recognized as the most common cause of sudden cardiac death that occurs in young people, including athletes. The clinical diagnosis is complemented with the ecocardiographic study, in which an abnormal myocardial hypertrophy of the septum can be observed in the absence of a cardiac or systemic disease (arterial systemic hypertension, aortic stenosis).