[Cochlear implant in hypoacusis with alteration of connexin 26].

Objective: The objective of this paper is to assess the benefits of cochlear implantation in a population of profound prelingual congenital deaf children with mutation of Connexin 26 (DFNB1 phenotype), compared with a population of profound congenital deaf children without mutation of this gene.

Patients And Method: This retrospective study was carried out in 36 children with cochlear implants under the age of 6. All had profound congenital bilateral sensorineural hearing impairment, without cochlear malformation.