Pseudotumor of the Maxillary Sinus in a Child with Von Willebrand Disease.

Introduction: Mandibular pseudotumors, also known as blood cysts, are rare complications which occur more frequently in patients with an associated bleeding disorder such as hemophilia.

Case Report: We present a case of a 2-year and 6-month-old patient with a hemophilic pseudotumor associated with Von Willebrand's disease, who consulted the emergency room due to spontaneous increase in volume of the left maxillary region, with no previous relevant medical history.

Conclusions: Different imaging studies were carried out to characterize the lesion, providing the necessary information for the correct approach.