[Cutaneous hemangiomas, vascular malformations and associated disorders. A new neurocutaneous syndrome].

Objective: Cutaneous hemangiomas and vascular malformations constitute a systemic disease that is the most frequent of the neurocutaneous syndromes reported to date. It appears more frequently in women than in men. The aim of this study was to describe the characteristics of this new neurocutaneous syndrome.

[Complex and complicated syndactylia. Review and treatment progress].

Complex syndactyly is generally defined as abnormal digital interconnection by bone, but sometimes simple syndactyly with complicated cutaneous, musculotendinous or neurovascular interconnections should be considered complex as well. Additionally, complex syndactyly involving anomalous bones (delta phalanx, brachiphalangism..

[Decrease in bacterial translocation in burned children treated with controlled nutritional support].

Introduction: Alteration in epithelial enteric cells are the main cause of bacteria translocation and local and systemic infections. Our aim is to evaluate these infections in burned children treated with enteral nutrition and compare the results with our previous observations. Material and methods.

[Integra Artificial dermis in pediatric reconstructive surgery].

Unlabelled: The recent release of artificial dermis for general use, has open wide a new field in pediatric reconstructive surgery. The aim of this paper is to analyze the results of Integra artificial dermis in our Plastic Surgery Department.

Materials And Methods: The records of the patients treated with Integra between february 1999 and january 2001 were analyzed, focusing on the indications, the complications and the final results.

[High flow vascular malformations in children].

Unlike hemangiomas and low-flow vascular malformations which are very common in children, arterial anomalies have small incidence. Differential diagnosis is difficult, and needs a physician familiarized with vascular anomalies. Appropriate treatment must be planned by multidisciplinary team considering the patient's age, and anatomical location.

Wet and dry deposition of 129I in Seville (Spain) measured by accelerator mass spectrometry.

Iodine-129 (T1/2 = 1.57 x 10(7) yr) concentrations have been determined by accelerator mass spectrometry in rainwater samples taken at Seville (southwestern Spain) in 1996 and 1997. This technique allows a reduction in the detection limits for this radionuclide in comparison to radiometric counting and other mass spectrometric methods such as ICP-MS.

Accelerator mass spectrometry as a powerful tool for the determination of 129I in rainwater.

129I is a very long-lived radionuclide (T(1/2) = 15.7 x 10(6) years) that is present in the environment both because of natural and anthropogenic sources. Its environmental interest, for example, as a tracer of geological processes, makes it the research target of a growing scientific community.

Determination of 129I in atmospheric samples by accelerator mass spectrometry.

A method for the radiochemical extraction of 129I from atmospheric charcoal filters and its measurement by accelerator mass spectrometry is presented. Either the 129I concentration or the 129I/127I atom ratio can be determined in the sample. With this method, air filters from Seville, in the Southwest of Spain (37.

[Resuscitation of the burned child in critical condition].

Recent advances in surgical techniques, control of infection and nutritional support have dramatically increased the survival rates of burned children. The characteristics of severely burned pediatric patients dictate that management be different from that required for adults in the intensive care unit. The formulas for fluid replacement should be based on body surface rather than weight in children and adjusted for degree of stress and age, with appropriate monitoring and treatment of hypothermia, pain and associated psychological disorders.

Venous graft repair following brachial artery thrombosis in a neonate.

A case of venous graft repair to recover blood flow of a newborn's upper extremity, is described. Even though this complication remains uncommon, we emphasize on to avoid brachial artery for vascular monitorization and to perform microsurgical revision as elective procedure if conservative therapy is unsuccessful.

[Hemangiomas and vascular malformations. Review and update].

In 1982, Mulliken and Glowacki classificated congenital vascular lesions in two biological groups with different treatment, evolution and prognosis: Haemangiomas and Vascular malformations. We have seen 230 patients, 145 with haemangiomas and 85 with vascular malformations (74 with low flow and 11 with high flow). We have reviewed clinical, evolutive and ecographic findings.

[Neutropenic enterocolitis in children with cancer].

Objectives: Neuropenic enterocolitis (NEC) is a destructive lesion of the ileocecal region occurring in cancer patients treated with chemotherapy. Its clinical picture is one of febrile acute abdominal extension with bloody diarrhea and low neutrophil counts. Our aim was to determine the incidence of NEC in children with cancer and to review the indications of surgery in these cases.

Costs of resistance: a test using transgenic Arabidopsis thaliana.

Evolutionary biologists have long attributed polymorphisms in resistance status to fitness costs of resistance traits. Nevertheless, pleiotropic fitness costs of resistance have been notoriously difficult to detect. We have transformed Arabidopsis thaliana with a mutant acetolactate synthase gene that confers resistance to the herbicide, chlorsulfuron.

[Congenital diaphragmatic hernia: an analysis of the results and prognostic factors prior to the development of an ECMO program].

Background: Some neonates with congenital diaphragmatic hernia (CDH) and persistent pulmonary hypertension are not adequately oxygenated with conventional treatment. The extracorporeal membrane oxygenation (ECMO) has been successful in some of them as an alternative in their management.

Patients And Methods: We studied the charts of 47 neonates with CDH, symptomatic within 24 hours of birth, treated in our institution during the last seven years (1987-1994).

Giant vascular malformation of the face in a premature infant: complete resolution by embolization.

The authors report on a neonate who had a large vascular malformation affecting the eye, maxilla, and mandible. This was managed successfully with percutaneous embolization.

Cultured epidermal autograft in the management of critical pediatric burn patients.

We treated 4 patients with CEA at "La Paz" Children's Hospital between July 1992 and September 1993. All of them had acute flame burns. The total body surface area (TBSA) of burn injury ranged from 75% to 85% with an age range of two to five years.

Biliary atresia and the polysplenia syndrome: its impact on final outcome.

Up to 25% of babies with biliary atresia (BA) bear associated malformations that most often cluster in the polysplenia syndrome (PS). This article examines the impact of associated PS on the final outcome of the authors' BA patients and the necessary modifications of surgical technique during orthotopic liver transplantation (OLT) in these patients. The authors studied 88 consecutive infants with biliary atresia operated upon during the 10-year period between 1984 and 1993.

[The usage of thermo-vac facial masks for the treatment of hypertrophic scars in children].

We present the results obtained in the treatment of facial hypertrophic scars in children admitted in the Pediatric Burn Unit of the Hospital Infantil La Paz (Madrid). During the last 30 months 13 patients, with ages ranging from 3 months to 5 years, have been treated. Compared to the elastic pressure masks, rigid masks have yielded better results both on the short and the long term.

[Portal venous flow as a prognostic factor in biliary atresia. A preliminary study].

Early prognosis factors determination is an important objective after Kasai's operation for biliary atresia repair. Serologic test, postoperative biliary flow, histologic studies and clinical manifestations provides adjunctive information. Hemodynamic patterns in biliary atresia where described in 80's before liver transplantation.

[A case of total intestinal aganglionosis. 2 years of survival].

A two-year-old male is presented. Small bowel aganglionosis was proved to extend to 3 cm below ligament of Treitz. Gastrostomy and ileostomy was done.