Objective: To highlight the possible association of intracranial aneurysm with autosomal recessive polycystic kidney disease.
Design, Setting, And Patient: To our knowledge, this association has been reported only twice in the medical literature. We herein report the case of a 21-year-old man with autosomal recessive polycystic kidney disease, presenting with subarachnoid hemorrhage secondary to a ruptured intracranial aneurysm, at our institution.