Venous Outflow and Otosclerosis: An Unusual Case of Pulsatile Tinnitus.

We report resolution of right-sided pulsatile tinnitus in a 44-year-old male who underwent stapedectomy for fenestral otosclerosis. Initial workup revealed a mixed hearing loss and absent stapedial reflexes consistent with ossicular fixation. CT angiography demonstrated near complete stenosis of the left-sided transverse and sigmoid sinuses and dominant contralateral venous outflow.

Long-Term Hearing Results of Endoskeletal Ossicular Reconstruction in Chronic Ears Using Titanium Prostheses Having a Helical Coil: Part 1-Kraus K-Helix Crown, Incus to Stapes.

Objectives: 1) To assess long-term hearing results after endoskeletal ossicular chain reconstruction (eOCR) using the titanium Kraus K-Helix Crown prosthesis, implanted incus to stapes, with glass-ionomer cement (GIC) in chronic ears and 2) to determine safety of the prosthesis and cement.

Study Design: Prospective, nonrandomized, sequential, single center, single surgeon.

Setting: Private practice, ambulatory surgical center.

Totally implantable hearing system: Five-year hearing results.

Objectives/hypothesis: 1) To provide long-term hearing outcome measures of a totally implantable hearing system (implant) and compare to the baseline unaided (BLU) and baseline aided (BLA) conditions, and 2) discuss relevant safety measures.

Study Design: Prospective, nonrandomized, multicenter, single-subject-as-own-control design.

Methods: Fifty-one subjects with mild to severe sensorineural hearing loss were implanted between 2008 and 2009 and enrolled in this postmarket approval study in the setting of private and hospital-based practices.

Profound high-frequency sensorineural hearing loss treatment with a totally implantable hearing system.

Objective: This study seeks to assess the efficacy of the Envoy Esteem totally implantable hearing device in treating profound high-frequency sensorineural hearing loss.

Patients: Five patients with profound high-frequency hearing loss participating in a prospective, multi-center, nonrandomized Food and Drug Administration clinical trial.

Intervention: Implantation with Esteem totally implantable hearing device and comparison to baseline unaided and aided conditions.

An unusual case of acute foot drop caused by a pseudoaneurysm.

Lower extremity neurologic symptoms are a common presenting problem. Here we report the case of a 73-year-old man who developed acute right foot pain and foot drop. History, physical examination, and electrodiagnostic studies were consistent with a lumbosacral plexopathy.

Envoy Esteem Totally Implantable Hearing System: phase 2 trial, 1-year hearing results.

Objectives: (1) To assess outcomes of the Envoy Esteem Totally Implantable Hearing System as measured by hearing results compared with preimplant baseline unaided (BLU) and best-fit aided conditions (BLA) and (2) to determine safety of the device.

Study Design: Prospective, nonrandomized, multicenter, subject-as-own-control, US Food and Drug Administration (FDA) trial.

Setting: Private practice and hospital-based.

Endoskeletal ossicular reconstruction using the Kraus K-Helix Crown and Piston middle ear prostheses.

The Kraus K-Helix Crown and Piston prostheses are novel, newly designed, MRI compatible, titanium ossicular replacement prostheses that have received U.S. Food and Drug Administration clearance in March of 2008 for ossiculoplasty.

Scaly, circular papules in a healthy toddler.

A 2-year-old boy presents with asymptomatic keratotic papules on his hands and feet. A biopsy is performed and he is confirmed to have punctate porokeratotic keratoderma. A discussion of punctate porokeratotic keratoderma is provided along with treatment options.

Medical malpractice and rhinology.

Background: Physicians facing malpractice litigation are in uncharted territory. The language, concepts, rules, and strategies of the legal system are foreign to science-based physicians. Understanding the statistics of rhinology malpractice litigation may aid the physician to cope with the assault of a claim.

Perivascular myoma of myopericytoma and myofibromatosis-type arising in a chronic scar.

We describe a case of a cutaneous perivascular myoma with features overlapping between the myofibromatosis and the myopericytoma type. The patient is a 58-year-old woman with a painless plaque-like and multinodular lesion in the pretibial dermis and subcutaneous tissue. She had repeated trauma to this site, first in her early youth that left an area of hyperpigmentation, and then again at age 40.

Bilateral anterior granulomatous uveitis associated with cutaneous Rosai-Dorfman disease.

Background: Rosai-Dorfman disease (RDD) is a benign, rare, histiocytic disorder of unknown etiology. We describe the case of a 61-year-old woman who presented to the ophthalmology clinic with bilateral granulomatous anterior uveitis.

Methods: The uveitis was controlled on topical prednisolone acetate 1%.

Cutaneous tumors as the initial presentation of non-T, non-B, nonmyeloid CD4+ CD56+ hematolymphoid malignancy in an adolescent boy.

We describe a 14-year-old Hispanic boy who presented with a 2-month history of enlarging plum-colored cutaneous tumors on his face, trunk, and proximal extremities. Histopathologic examination showed nodular infiltrates of malignant mononuclear cells extending from the superficial dermis to the deep subcutis. Immunohistochemical staining of the biopsy specimen and flow cytometry studies on a bone marrow aspirate revealed a CD4+, CD56+ hematolymphoid tumor that was negative for all other myeloid and lymphoid markers.

Paraneoplastic movement disorder in a patient with non-Hodgkin's lymphoma and CRMP-5 autoantibody.

The paraneoplastic autoantibody, collapsin response-mediator protein (CRMP)-5 immunoglobulin G (IgG), is specific for neuronal cytoplasmic CRMP-5, and is usually associated with small-cell lung carcinoma or thymoma. We report on details of a movement disorder that followed anti-B-cell therapy in a patient with lymphoma, and was accompanied by CRMP-5 IgG.

Adult onset of eruptive widespread Spitz's nevi.

Cases of multiple Spitz's nevi are rare, usually occurring in the agminate form or even less commonly as widespread eruptive Spitz's nevi. Previously reported cases of widespread eruptive Spitz's nevi arose in persons age 23 or younger. We describe a Hispanic male patient with eruptive Spitz's nevi that presented at the age of 35 years.