Portopulmonary hypertension: hemodynamics, pulmonary angiography, and configuration of the heart.

Background: The goal of the present study was to examine the cardiac configuration and pulmonary vascular changes in patients with portopulmonary hypertension (PPHTN) and compare them with those of idiopathic pulmonary arterial hypertension (IPAH).

Methods And Results: The subjects were 10 patients with PPHTN and 18 with IPAH. In PPHTN, the increases in the right ventricular end-diastolic volume index (89+/-19 vs 128+/-50 ml/m2; p=0.

Efficacy of acute inhalation of nitric oxide in patients with primary pulmonary hypertension using chronic use of continuous epoprostenol infusion.

Background: There have only been a few reports published on combination therapy for patients with primary pulmonary hypertension (PPH).

Methods And Results: Fifteen patients with PPH (4 men and 11 women, 34.5+/-12.