Total knee replacement in Osteogenesis Imperfecta: a case report and review of the literature.

Background: A review of the literature revealed that only 9 total knee replacements were performed on patients with osteogenesis imperfecta (OI), with one being a revision procedure of a periprosthetic fracture. Of the 9 primary procedures, all used cemented prostheses, and 3 patients had an osteotomy at the same procedure. Our patient required a hinged prosthesis because of collateral ligament incompetence and is the first such case reported in the literature.

Hip Arthroplasty in Patients with Osteogenesis Imperfecta.

»: Osteogenesis imperfecta (OI) is a rare congenital disorder that affects connective tissue.

»: Modern medicine has mitigated the mortality that is associated with OI, allowing patients to live a near-normal life span.

»: The degenerative process in OI is probably accelerated because of subclinical intra-articular fractures, joint laxity, and distorted femoral and acetabular anatomy.