Publications by authors named "K de Potocki"

Article Synopsis
  • The study investigates the occurrence of organ damage in patients with childhood-onset systemic lupus erythematosus (cSLE) and aims to predict when this damage might occur.
  • A total of 97 patients were followed over 29 years, revealing that 48% had organ damage by the last follow-up, with findings indicating that significant damage is unlikely within the first 6 years post-diagnosis for half of the patients.
  • Higher initial disease severity scores and increased glucocorticoid treatment were linked to faster damage accumulation, suggesting that monitoring and treatment strategies should be adjusted based on specific risk factors.
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The major event that hit Europe in summer 2021 reminds society that floods are recurrent and among the costliest and deadliest natural hazards. The long-term flood risk management (FRM) efforts preferring sole technical measures to prevent and mitigate floods have shown to be not sufficiently effective and sensitive to the environment. Nature-Based Solutions (NBS) mark a recent paradigm shift of FRM towards solutions that use nature-derived features, processes and management options to improve water retention and mitigate floods.

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The three common alleles of the gene, ɛ2/ɛ3/ɛ4, have been linked to human spatial orientation. We investigated the genetic role of in developmental topographical disorientation (DTD), a lifelong condition that results in topographical disorientation. We genotyped the ɛ2/ɛ3/ɛ4 alleles in a cohort of 20 unrelated DTD probands, and found allele frequencies not statistically different from the those seen in the population as a whole.

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Introduction/objectives: Magnetic resonance imaging (MRI) is recommended for evaluation of changes in juvenile spondyloarthropathies (JSpA). To our knowledge, there is no previous prospective study analysing early changes on axial MRI. The objective is to investigate incidence of reparable changes on axial MRI in patients with established JSpA, lasting for less than 6 months.

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Uveitis (JIA-U), the most common extra-articular manifestation in juvenile idiopathic arthritis (JIA), may cause severe impairment of vision in children and affect their quality of life (QoL). Considering the lack of uveitis-related QoL assessment questionnaire, and multidimensional nature of the Juvenile Arthritis Multidimensional Assessment Report (JAMAR), commonly used for monitoring and assessing the health status of children with JIA, we performed a cross-sectional study to investigate the potential of the JAMAR in estimation of QoL in children suffering from JIA-U. The study included 42 children with JIA, 21 of whom had JIA-U.

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