Perivascular epithelioid cell tumor (PEComa) of the liver. An extremely rare diagnosis.

Hepatic PEComa are tumors that show perivascular epithelioid cell differentiation. Scarcely published, its management is based on small case series and currently its treatment of choice is surgical resection. We present a clinical case of a 74-year-old woman who underwent surgery at our hospital for a benign hepatic PEComa.